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Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report

INTRODUCTION: Synovial sarcoma is a malignant tumour of mesenchymal origin with an aggressive character and a rare cervicofacial location. Its management is multidisciplinary in order to improve prognosis and survival. CASE REPORT: We report the case of two rare and synchronous localizations of mono...

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Autores principales: Sabr, Ayoub, Azami Hassani, Fatema Ez-zahrae, Iro, Salissou, Slimani, Faiçal
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8234347/
https://www.ncbi.nlm.nih.gov/pubmed/34194735
http://dx.doi.org/10.1016/j.amsu.2021.102523
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author Sabr, Ayoub
Azami Hassani, Fatema Ez-zahrae
Iro, Salissou
Slimani, Faiçal
author_facet Sabr, Ayoub
Azami Hassani, Fatema Ez-zahrae
Iro, Salissou
Slimani, Faiçal
author_sort Sabr, Ayoub
collection PubMed
description INTRODUCTION: Synovial sarcoma is a malignant tumour of mesenchymal origin with an aggressive character and a rare cervicofacial location. Its management is multidisciplinary in order to improve prognosis and survival. CASE REPORT: We report the case of two rare and synchronous localizations of monophasic synovial sarcoma of the maxilla and chest wall in a 58-year-old woman, whose management was based on exclusive chemotherapy. DISCUSSION: The cervicofacial location of synovial sarcoma represents 3% of all locations in the body. Its clinical and radiological manifestations are aspecific. Its diagnosis is based on a combination of histological and genetic arguments. Its therapeutic management depends on the tumour stage and prognostic factors. CONCLUSION: Early diagnosis of cervicofacial synovial sarcoma allows to avoid a mutilating procedure for the patient and to improve the long-term prognosis by a good control of the tumour.
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spelling pubmed-82343472021-06-29 Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report Sabr, Ayoub Azami Hassani, Fatema Ez-zahrae Iro, Salissou Slimani, Faiçal Ann Med Surg (Lond) Case Report INTRODUCTION: Synovial sarcoma is a malignant tumour of mesenchymal origin with an aggressive character and a rare cervicofacial location. Its management is multidisciplinary in order to improve prognosis and survival. CASE REPORT: We report the case of two rare and synchronous localizations of monophasic synovial sarcoma of the maxilla and chest wall in a 58-year-old woman, whose management was based on exclusive chemotherapy. DISCUSSION: The cervicofacial location of synovial sarcoma represents 3% of all locations in the body. Its clinical and radiological manifestations are aspecific. Its diagnosis is based on a combination of histological and genetic arguments. Its therapeutic management depends on the tumour stage and prognostic factors. CONCLUSION: Early diagnosis of cervicofacial synovial sarcoma allows to avoid a mutilating procedure for the patient and to improve the long-term prognosis by a good control of the tumour. Elsevier 2021-06-20 /pmc/articles/PMC8234347/ /pubmed/34194735 http://dx.doi.org/10.1016/j.amsu.2021.102523 Text en © 2021 Published by Elsevier Ltd on behalf of IJS Publishing Group Ltd. https://creativecommons.org/licenses/by/4.0/This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Sabr, Ayoub
Azami Hassani, Fatema Ez-zahrae
Iro, Salissou
Slimani, Faiçal
Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report
title Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report
title_full Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report
title_fullStr Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report
title_full_unstemmed Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report
title_short Synovial sarcoma of the maxillary sinus and chest wall: An exceptional association of two synchronous rare locations, Case report
title_sort synovial sarcoma of the maxillary sinus and chest wall: an exceptional association of two synchronous rare locations, case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8234347/
https://www.ncbi.nlm.nih.gov/pubmed/34194735
http://dx.doi.org/10.1016/j.amsu.2021.102523
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