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Gastric Adenocarcinoma in the Setting of IPEX Syndrome

Immune dysregulation, polyendocrinopathy, enteropathy, X-linked (IPEX) syndrome is a rare X-linked disorder caused by a loss of function mutation in the FOXP3 gene. It manifests early in infancy with clinical symptoms including autoimmune enteropathy, type 1 diabetes mellitus, and eczema. While aber...

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Detalles Bibliográficos
Autores principales:	Steffin, David, Bhar, Saleh, Fishman, Douglas S., Rider, Nicholas L., Naik-Mathuria, Bindi, Martinez, Caridad, Venkatramani, Rajkumar
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2021
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8257369/ https://www.ncbi.nlm.nih.gov/pubmed/34258086 http://dx.doi.org/10.1155/2021/9967198

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