An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration

A 42-year-old woman visited our hospital due to syncope. Contrast-enhanced CT revealed portosystemic shunt, portal vein hypoplasia, and multiple liver nodules. The histological examination of a liver biopsy specimen exhibited portal vein hypoplasia and revealed that the liver tumor was positive for...

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Autores principales: Tanaka, Hironori, Saijo, Yoshihito, Tomonari, Tetsu, Tanaka, Takahiro, Taniguchi, Tatsuya, Yagi, Shusuke, Okamoto, Koichi, Miyamoto, Hiroshi, Sogabe, Masahiro, Sato, Yasushi, Muguruma, Naoki, Tsuneyama, Koichi, Sata, Masataka, Takayama, Tetsuji
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Internal Medicine 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8263181/
https://www.ncbi.nlm.nih.gov/pubmed/33456037
http://dx.doi.org/10.2169/internalmedicine.5914-20
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author Tanaka, Hironori
Saijo, Yoshihito
Tomonari, Tetsu
Tanaka, Takahiro
Taniguchi, Tatsuya
Yagi, Shusuke
Okamoto, Koichi
Miyamoto, Hiroshi
Sogabe, Masahiro
Sato, Yasushi
Muguruma, Naoki
Tsuneyama, Koichi
Sata, Masataka
Takayama, Tetsuji
author_facet Tanaka, Hironori
Saijo, Yoshihito
Tomonari, Tetsu
Tanaka, Takahiro
Taniguchi, Tatsuya
Yagi, Shusuke
Okamoto, Koichi
Miyamoto, Hiroshi
Sogabe, Masahiro
Sato, Yasushi
Muguruma, Naoki
Tsuneyama, Koichi
Sata, Masataka
Takayama, Tetsuji
author_sort Tanaka, Hironori
collection PubMed
description A 42-year-old woman visited our hospital due to syncope. Contrast-enhanced CT revealed portosystemic shunt, portal vein hypoplasia, and multiple liver nodules. The histological examination of a liver biopsy specimen exhibited portal vein hypoplasia and revealed that the liver tumor was positive for glutamine synthetase. The patient was therefore diagnosed with congenital extrahepatic portosystemic shunt type II, and with focal nodular hyperplasia (FNH)-like nodules. She had the complication of severe portopulmonary hypertension and underwent complete shunt closure by balloon-occluded retrograde transvenous obliteration (B-RTO). The intrahepatic portal vein was well developed at 1 year after B-RTO, and multiple liver nodules completely regressed. Her pulmonary hypertension also improved.
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spelling pubmed-82631812021-07-12 An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration Tanaka, Hironori Saijo, Yoshihito Tomonari, Tetsu Tanaka, Takahiro Taniguchi, Tatsuya Yagi, Shusuke Okamoto, Koichi Miyamoto, Hiroshi Sogabe, Masahiro Sato, Yasushi Muguruma, Naoki Tsuneyama, Koichi Sata, Masataka Takayama, Tetsuji Intern Med Case Report A 42-year-old woman visited our hospital due to syncope. Contrast-enhanced CT revealed portosystemic shunt, portal vein hypoplasia, and multiple liver nodules. The histological examination of a liver biopsy specimen exhibited portal vein hypoplasia and revealed that the liver tumor was positive for glutamine synthetase. The patient was therefore diagnosed with congenital extrahepatic portosystemic shunt type II, and with focal nodular hyperplasia (FNH)-like nodules. She had the complication of severe portopulmonary hypertension and underwent complete shunt closure by balloon-occluded retrograde transvenous obliteration (B-RTO). The intrahepatic portal vein was well developed at 1 year after B-RTO, and multiple liver nodules completely regressed. Her pulmonary hypertension also improved. The Japanese Society of Internal Medicine 2021-01-15 2021-06-15 /pmc/articles/PMC8263181/ /pubmed/33456037 http://dx.doi.org/10.2169/internalmedicine.5914-20 Text en Copyright © 2021 by The Japanese Society of Internal Medicine https://creativecommons.org/licenses/by-nc-nd/4.0/The Internal Medicine is an Open Access journal distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Tanaka, Hironori
Saijo, Yoshihito
Tomonari, Tetsu
Tanaka, Takahiro
Taniguchi, Tatsuya
Yagi, Shusuke
Okamoto, Koichi
Miyamoto, Hiroshi
Sogabe, Masahiro
Sato, Yasushi
Muguruma, Naoki
Tsuneyama, Koichi
Sata, Masataka
Takayama, Tetsuji
An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration
title An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration
title_full An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration
title_fullStr An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration
title_full_unstemmed An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration
title_short An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration
title_sort adult case of congenital extrahepatic portosystemic shunt successfully treated with balloon-occluded retrograde transvenous obliteration
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8263181/
https://www.ncbi.nlm.nih.gov/pubmed/33456037
http://dx.doi.org/10.2169/internalmedicine.5914-20
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