IgG4-related sclerosing cholangitis: not always an obvious entity

Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinom...

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Detalles Bibliográficos
Autores principales: Velegraki, Magdalini, Vardas, Emmanouil, Dervenis, Christos, Fragaki, Maria, Nikolaou, Pinelopi, Mpitouli, Afroditi, Kazamias, George, Sepsa, Athanasia, Giannikaki, Elpida, Paspatis, Gregorios A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hellenic Society of Gastroenterology 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8276355/
https://www.ncbi.nlm.nih.gov/pubmed/34276201
http://dx.doi.org/10.20524/aog.2021.0610
Descripción
Sumario:Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinoma. This case highlights that differentiating between isolated IgG4-SC and cholangiocarcinoma can present a challenging diagnostic dilemma.

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