IgG4-related sclerosing cholangitis: not always an obvious entity

Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinom...

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Autores principales: Velegraki, Magdalini, Vardas, Emmanouil, Dervenis, Christos, Fragaki, Maria, Nikolaou, Pinelopi, Mpitouli, Afroditi, Kazamias, George, Sepsa, Athanasia, Giannikaki, Elpida, Paspatis, Gregorios A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hellenic Society of Gastroenterology 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8276355/
https://www.ncbi.nlm.nih.gov/pubmed/34276201
http://dx.doi.org/10.20524/aog.2021.0610
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author Velegraki, Magdalini
Vardas, Emmanouil
Dervenis, Christos
Fragaki, Maria
Nikolaou, Pinelopi
Mpitouli, Afroditi
Kazamias, George
Sepsa, Athanasia
Giannikaki, Elpida
Paspatis, Gregorios A.
author_facet Velegraki, Magdalini
Vardas, Emmanouil
Dervenis, Christos
Fragaki, Maria
Nikolaou, Pinelopi
Mpitouli, Afroditi
Kazamias, George
Sepsa, Athanasia
Giannikaki, Elpida
Paspatis, Gregorios A.
author_sort Velegraki, Magdalini
collection PubMed
description Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinoma. This case highlights that differentiating between isolated IgG4-SC and cholangiocarcinoma can present a challenging diagnostic dilemma.
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spelling pubmed-82763552021-07-16 IgG4-related sclerosing cholangitis: not always an obvious entity Velegraki, Magdalini Vardas, Emmanouil Dervenis, Christos Fragaki, Maria Nikolaou, Pinelopi Mpitouli, Afroditi Kazamias, George Sepsa, Athanasia Giannikaki, Elpida Paspatis, Gregorios A. Ann Gastroenterol Case Report Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinoma. This case highlights that differentiating between isolated IgG4-SC and cholangiocarcinoma can present a challenging diagnostic dilemma. Hellenic Society of Gastroenterology 2021 2021-02-26 /pmc/articles/PMC8276355/ /pubmed/34276201 http://dx.doi.org/10.20524/aog.2021.0610 Text en Copyright: © Hellenic Society of Gastroenterology https://creativecommons.org/licenses/by-nc-sa/3.0/This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Velegraki, Magdalini
Vardas, Emmanouil
Dervenis, Christos
Fragaki, Maria
Nikolaou, Pinelopi
Mpitouli, Afroditi
Kazamias, George
Sepsa, Athanasia
Giannikaki, Elpida
Paspatis, Gregorios A.
IgG4-related sclerosing cholangitis: not always an obvious entity
title IgG4-related sclerosing cholangitis: not always an obvious entity
title_full IgG4-related sclerosing cholangitis: not always an obvious entity
title_fullStr IgG4-related sclerosing cholangitis: not always an obvious entity
title_full_unstemmed IgG4-related sclerosing cholangitis: not always an obvious entity
title_short IgG4-related sclerosing cholangitis: not always an obvious entity
title_sort igg4-related sclerosing cholangitis: not always an obvious entity
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8276355/
https://www.ncbi.nlm.nih.gov/pubmed/34276201
http://dx.doi.org/10.20524/aog.2021.0610
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