Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter

Anorectal malformation with rectovestibular fistula associated with vaginal agenesis is rare. We report on a child in whom this combination was diagnosed at the age of 1 year. After creation of a divided descending colostomy, we chose to leave the rectum-rectovestibular fistula to function as a neov...

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Autores principales: Dessanti, Antonio, Louisma, Osnel, Pierre, Gabriel Steve, Liem, Nguhien Thanh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Georg Thieme Verlag KG 2021
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8276751/
https://www.ncbi.nlm.nih.gov/pubmed/34277324
http://dx.doi.org/10.1055/s-0041-1728725
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author Dessanti, Antonio
Louisma, Osnel
Pierre, Gabriel Steve
Liem, Nguhien Thanh
author_facet Dessanti, Antonio
Louisma, Osnel
Pierre, Gabriel Steve
Liem, Nguhien Thanh
author_sort Dessanti, Antonio
collection PubMed
description Anorectal malformation with rectovestibular fistula associated with vaginal agenesis is rare. We report on a child in whom this combination was diagnosed at the age of 1 year. After creation of a divided descending colostomy, we chose to leave the rectum-rectovestibular fistula to function as a neovagina, while the sigmoid colon was relocated via modified posterior sagittal anorectoplasty. The colostomy was closed 6 months after the main surgery. After a follow-up of 3 years, the patient is continent for stool and urine. The introitus of the neovagina appears wide and easy to explore. We conclude that our surgical approach may be a good option for these children.
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spelling pubmed-82767512021-07-16 Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter Dessanti, Antonio Louisma, Osnel Pierre, Gabriel Steve Liem, Nguhien Thanh European J Pediatr Surg Rep Anorectal malformation with rectovestibular fistula associated with vaginal agenesis is rare. We report on a child in whom this combination was diagnosed at the age of 1 year. After creation of a divided descending colostomy, we chose to leave the rectum-rectovestibular fistula to function as a neovagina, while the sigmoid colon was relocated via modified posterior sagittal anorectoplasty. The colostomy was closed 6 months after the main surgery. After a follow-up of 3 years, the patient is continent for stool and urine. The introitus of the neovagina appears wide and easy to explore. We conclude that our surgical approach may be a good option for these children. Georg Thieme Verlag KG 2021-01 2021-07-12 /pmc/articles/PMC8276751/ /pubmed/34277324 http://dx.doi.org/10.1055/s-0041-1728725 Text en The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. ( https://creativecommons.org/licenses/by/4.0/ ) https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Dessanti, Antonio
Louisma, Osnel
Pierre, Gabriel Steve
Liem, Nguhien Thanh
Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter
title Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter
title_full Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter
title_fullStr Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter
title_full_unstemmed Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter
title_short Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter
title_sort anorectal malformation with rectovestibular fistula and vaginal agenesis: usage of rectovestibular fistula as a neovagina followed by psarp with preservation of the anal sphincter
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8276751/
https://www.ncbi.nlm.nih.gov/pubmed/34277324
http://dx.doi.org/10.1055/s-0041-1728725
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