A Long-Term Survivor With Alveolar Capillary Dysplasia

A patient with alveolar capillary dysplasia has survived more than 56 months with medical therapy. Intrauterine exposure to metformin potentially modified the severity of disease. In combination with other agents, endothelin receptor antagonists and amlodipine have been key medications in lowering p...

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Detalles Bibliográficos
Autores principales: Yost, Chandler E., Putnam, Angelica R., Dishop, Megan K., Jorgensen, Lynda O., Wirkus, Paul E., Day, Ronald W.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Mini-Focus Issue: Heart Failure
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8302120/
https://www.ncbi.nlm.nih.gov/pubmed/34317003
http://dx.doi.org/10.1016/j.jaccas.2020.05.055
Descripción
Sumario:A patient with alveolar capillary dysplasia has survived more than 56 months with medical therapy. Intrauterine exposure to metformin potentially modified the severity of disease. In combination with other agents, endothelin receptor antagonists and amlodipine have been key medications in lowering pulmonary arterial pressure and managing right heart failure. (Level of Difficulty: Beginner.)

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