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Perturbation of semaphorin and VEGF signaling in ACDMPV lungs due to FOXF1 deficiency
BACKGROUND: Alveolar capillary dysplasia with misalignment of pulmonary veins (ACDMPV) is a rare lethal congenital lung disorder in neonates characterized by severe progressive respiratory failure and refractory pulmonary hypertension, resulting from underdevelopment of the peripheral pulmonary tree...
Autores principales: | Karolak, Justyna A., Gambin, Tomasz, Szafranski, Przemyslaw, Maywald, Rebecca L., Popek, Edwina, Heaney, Jason D., Stankiewicz, Paweł |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8314029/ https://www.ncbi.nlm.nih.gov/pubmed/34315444 http://dx.doi.org/10.1186/s12931-021-01797-7 |
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