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Distinct Mitochondrial Pathologies Caused by Mutations of the Proximal Tubular Enzymes EHHADH and GATM

The mitochondria of the proximal tubule are essential for providing energy in this nephron segment, whose ATP generation is almost exclusively oxygen dependent. In addition, mitochondria are involved in a variety of metabolic processes and complex signaling networks. Proximal tubular mitochondrial d...

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Detalles Bibliográficos
Autores principales:	Forst, Anna-Lena, Reichold, Markus, Kleta, Robert, Warth, Richard
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2021
Materias:	Physiology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8326905/ https://www.ncbi.nlm.nih.gov/pubmed/34349672 http://dx.doi.org/10.3389/fphys.2021.715485

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