Congenital epignathus associated with a cleft palate: a case report

BACKGROUND: Epignathus is a rare, benign, congenital teratoma of the hard palate with an estimated incidence of 1 in 200,000 live births. Epignathus frequently leads to a high mortality (80–100%) due to airway obstruction in the neonatal period. CASE PRESENTATION: We report a case of successful mana...

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Detalles Bibliográficos
Autores principales: Lele Mutombo, Fabrice, Nzanzu Kikuhe, Jason, Kasereka Mwanamolo, Noé, Erickson, Marc H., Wetzig, Neil, Kabuyaya Kakule, Médard
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8330006/
https://www.ncbi.nlm.nih.gov/pubmed/34340710
http://dx.doi.org/10.1186/s13256-021-03007-w
Descripción
Sumario:BACKGROUND: Epignathus is a rare, benign, congenital teratoma of the hard palate with an estimated incidence of 1 in 200,000 live births. Epignathus frequently leads to a high mortality (80–100%) due to airway obstruction in the neonatal period. CASE PRESENTATION: We report a case of successful management of a rare oropharyngeal teratoma in a African newborn girl who was referred to our institute with a large protruding intraoral mass, combined with cleft palate, causing some respiratory compromise. The palatal mass was removed on the fifth day after birth, and a palatoplasty performed on day 30. CONCLUSION: Epignathus is a life-threatening condition at the time of delivery. Appropriate management begins with securing the airway, followed by complete resection of the tumor.

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