Cargando…

“West Syndrome—Infantile Spasms”: A Pediatric Case Report

West syndrome is a rare, severe form of epilepsy with onset in infancy and early childhood. It combines episodes of epileptic spasms that occur in a cluster, an abnormal pattern of interictal electroencephalogram termed as hypsarrhythmia and neuropsychomotor delay. The syndrome mainly results from b...

Descripción completa

Detalles Bibliográficos
Autores principales: Goswami, Mridula, Sharma, Sadhna
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Jaypee Brothers Medical Publishers 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8343679/
https://www.ncbi.nlm.nih.gov/pubmed/34413615
http://dx.doi.org/10.5005/jp-journals-10005-1922
_version_ 1783734334285414400
author Goswami, Mridula
Sharma, Sadhna
author_facet Goswami, Mridula
Sharma, Sadhna
author_sort Goswami, Mridula
collection PubMed
description West syndrome is a rare, severe form of epilepsy with onset in infancy and early childhood. It combines episodes of epileptic spasms that occur in a cluster, an abnormal pattern of interictal electroencephalogram termed as hypsarrhythmia and neuropsychomotor delay. The syndrome mainly results from brain dysfunction in the prenatal, perinatal, or postnatal period and focal lesions early in life may secondarily affect other sites in the brain presenting with some degree of developmental delay and mental retardation. The oral manifestations vary to a large extent presenting as generalized tooth wear, gingival enlargement, multiple white spot lesions, and a high-arched palate. This case report highlights the importance of early diagnosis, various clinical features, and management in a pediatric patient with West syndrome. How to cite this article: Goswami M, Sharma S. “West Syndrome—Infantile Spasms”: A Pediatric Case Report. Int J Clin Pediatr Dent 2021;14(2):323–326.
format Online
Article
Text
id pubmed-8343679
institution National Center for Biotechnology Information
language English
publishDate 2021
publisher Jaypee Brothers Medical Publishers
record_format MEDLINE/PubMed
spelling pubmed-83436792021-08-18 “West Syndrome—Infantile Spasms”: A Pediatric Case Report Goswami, Mridula Sharma, Sadhna Int J Clin Pediatr Dent Case Report West syndrome is a rare, severe form of epilepsy with onset in infancy and early childhood. It combines episodes of epileptic spasms that occur in a cluster, an abnormal pattern of interictal electroencephalogram termed as hypsarrhythmia and neuropsychomotor delay. The syndrome mainly results from brain dysfunction in the prenatal, perinatal, or postnatal period and focal lesions early in life may secondarily affect other sites in the brain presenting with some degree of developmental delay and mental retardation. The oral manifestations vary to a large extent presenting as generalized tooth wear, gingival enlargement, multiple white spot lesions, and a high-arched palate. This case report highlights the importance of early diagnosis, various clinical features, and management in a pediatric patient with West syndrome. How to cite this article: Goswami M, Sharma S. “West Syndrome—Infantile Spasms”: A Pediatric Case Report. Int J Clin Pediatr Dent 2021;14(2):323–326. Jaypee Brothers Medical Publishers 2021 /pmc/articles/PMC8343679/ /pubmed/34413615 http://dx.doi.org/10.5005/jp-journals-10005-1922 Text en Copyright © 2021; Jaypee Brothers Medical Publishers (P) Ltd. https://creativecommons.org/licenses/by-nc/4.0/© Jaypee Brothers Medical Publishers. 2021 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (https://creativecommons.org/licenses/by-nc/4.0/), which permits unrestricted use, distribution, and non-commercial reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/ (https://creativecommons.org/publicdomain/zero/1.0/) ) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Goswami, Mridula
Sharma, Sadhna
“West Syndrome—Infantile Spasms”: A Pediatric Case Report
title “West Syndrome—Infantile Spasms”: A Pediatric Case Report
title_full “West Syndrome—Infantile Spasms”: A Pediatric Case Report
title_fullStr “West Syndrome—Infantile Spasms”: A Pediatric Case Report
title_full_unstemmed “West Syndrome—Infantile Spasms”: A Pediatric Case Report
title_short “West Syndrome—Infantile Spasms”: A Pediatric Case Report
title_sort “west syndrome—infantile spasms”: a pediatric case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8343679/
https://www.ncbi.nlm.nih.gov/pubmed/34413615
http://dx.doi.org/10.5005/jp-journals-10005-1922
work_keys_str_mv AT goswamimridula westsyndromeinfantilespasmsapediatriccasereport
AT sharmasadhna westsyndromeinfantilespasmsapediatriccasereport