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“West Syndrome—Infantile Spasms”: A Pediatric Case Report
West syndrome is a rare, severe form of epilepsy with onset in infancy and early childhood. It combines episodes of epileptic spasms that occur in a cluster, an abnormal pattern of interictal electroencephalogram termed as hypsarrhythmia and neuropsychomotor delay. The syndrome mainly results from b...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Jaypee Brothers Medical Publishers
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8343679/ https://www.ncbi.nlm.nih.gov/pubmed/34413615 http://dx.doi.org/10.5005/jp-journals-10005-1922 |
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author | Goswami, Mridula Sharma, Sadhna |
author_facet | Goswami, Mridula Sharma, Sadhna |
author_sort | Goswami, Mridula |
collection | PubMed |
description | West syndrome is a rare, severe form of epilepsy with onset in infancy and early childhood. It combines episodes of epileptic spasms that occur in a cluster, an abnormal pattern of interictal electroencephalogram termed as hypsarrhythmia and neuropsychomotor delay. The syndrome mainly results from brain dysfunction in the prenatal, perinatal, or postnatal period and focal lesions early in life may secondarily affect other sites in the brain presenting with some degree of developmental delay and mental retardation. The oral manifestations vary to a large extent presenting as generalized tooth wear, gingival enlargement, multiple white spot lesions, and a high-arched palate. This case report highlights the importance of early diagnosis, various clinical features, and management in a pediatric patient with West syndrome. How to cite this article: Goswami M, Sharma S. “West Syndrome—Infantile Spasms”: A Pediatric Case Report. Int J Clin Pediatr Dent 2021;14(2):323–326. |
format | Online Article Text |
id | pubmed-8343679 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Jaypee Brothers Medical Publishers |
record_format | MEDLINE/PubMed |
spelling | pubmed-83436792021-08-18 “West Syndrome—Infantile Spasms”: A Pediatric Case Report Goswami, Mridula Sharma, Sadhna Int J Clin Pediatr Dent Case Report West syndrome is a rare, severe form of epilepsy with onset in infancy and early childhood. It combines episodes of epileptic spasms that occur in a cluster, an abnormal pattern of interictal electroencephalogram termed as hypsarrhythmia and neuropsychomotor delay. The syndrome mainly results from brain dysfunction in the prenatal, perinatal, or postnatal period and focal lesions early in life may secondarily affect other sites in the brain presenting with some degree of developmental delay and mental retardation. The oral manifestations vary to a large extent presenting as generalized tooth wear, gingival enlargement, multiple white spot lesions, and a high-arched palate. This case report highlights the importance of early diagnosis, various clinical features, and management in a pediatric patient with West syndrome. How to cite this article: Goswami M, Sharma S. “West Syndrome—Infantile Spasms”: A Pediatric Case Report. Int J Clin Pediatr Dent 2021;14(2):323–326. Jaypee Brothers Medical Publishers 2021 /pmc/articles/PMC8343679/ /pubmed/34413615 http://dx.doi.org/10.5005/jp-journals-10005-1922 Text en Copyright © 2021; Jaypee Brothers Medical Publishers (P) Ltd. https://creativecommons.org/licenses/by-nc/4.0/© Jaypee Brothers Medical Publishers. 2021 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (https://creativecommons.org/licenses/by-nc/4.0/), which permits unrestricted use, distribution, and non-commercial reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/ (https://creativecommons.org/publicdomain/zero/1.0/) ) applies to the data made available in this article, unless otherwise stated. |
spellingShingle | Case Report Goswami, Mridula Sharma, Sadhna “West Syndrome—Infantile Spasms”: A Pediatric Case Report |
title | “West Syndrome—Infantile Spasms”: A Pediatric Case Report |
title_full | “West Syndrome—Infantile Spasms”: A Pediatric Case Report |
title_fullStr | “West Syndrome—Infantile Spasms”: A Pediatric Case Report |
title_full_unstemmed | “West Syndrome—Infantile Spasms”: A Pediatric Case Report |
title_short | “West Syndrome—Infantile Spasms”: A Pediatric Case Report |
title_sort | “west syndrome—infantile spasms”: a pediatric case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8343679/ https://www.ncbi.nlm.nih.gov/pubmed/34413615 http://dx.doi.org/10.5005/jp-journals-10005-1922 |
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