Cargando…
Congenital infantile digital fibromatosis: a case report and review of the literature
Infantile digital fibromatosis (IDF), also called inclusion body fibromatosis is an uncommon benign tumour occurring in the digits of young children. In about a third of cases, it is congenital and the diagnosis is based on the presence of peculiar intracytoplasmic inclusions on histology. Recurrenc...
Autores principales: | , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Makerere Medical School
2020
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8351811/ https://www.ncbi.nlm.nih.gov/pubmed/34394250 http://dx.doi.org/10.4314/ahs.v20i4.42 |
_version_ | 1783736049985388544 |
---|---|
author | Adegoke, Omolade O Ajao, Akinlabi E Ano-Edward, Gbemi H |
author_facet | Adegoke, Omolade O Ajao, Akinlabi E Ano-Edward, Gbemi H |
author_sort | Adegoke, Omolade O |
collection | PubMed |
description | Infantile digital fibromatosis (IDF), also called inclusion body fibromatosis is an uncommon benign tumour occurring in the digits of young children. In about a third of cases, it is congenital and the diagnosis is based on the presence of peculiar intracytoplasmic inclusions on histology. Recurrence rate post-surgery is high. However, spontaneous regression has been reported. We present a case of a 5-month-old infant who had excision of a right second toe mass, which has been present from birth. Histological examination revealed this to be infantile digital fibromatosis. To the best of our knowledge, no report of this has been made in Nigeria. It is important that this diagnosis be entertained in young children with masses on the digits as this will influence the management instituted. |
format | Online Article Text |
id | pubmed-8351811 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2020 |
publisher | Makerere Medical School |
record_format | MEDLINE/PubMed |
spelling | pubmed-83518112021-08-12 Congenital infantile digital fibromatosis: a case report and review of the literature Adegoke, Omolade O Ajao, Akinlabi E Ano-Edward, Gbemi H Afr Health Sci Articles Infantile digital fibromatosis (IDF), also called inclusion body fibromatosis is an uncommon benign tumour occurring in the digits of young children. In about a third of cases, it is congenital and the diagnosis is based on the presence of peculiar intracytoplasmic inclusions on histology. Recurrence rate post-surgery is high. However, spontaneous regression has been reported. We present a case of a 5-month-old infant who had excision of a right second toe mass, which has been present from birth. Histological examination revealed this to be infantile digital fibromatosis. To the best of our knowledge, no report of this has been made in Nigeria. It is important that this diagnosis be entertained in young children with masses on the digits as this will influence the management instituted. Makerere Medical School 2020-12 /pmc/articles/PMC8351811/ /pubmed/34394250 http://dx.doi.org/10.4314/ahs.v20i4.42 Text en © 2020 Adegoke OO et al. https://creativecommons.org/licenses/by/4.0/Licensee African Health Sciences. This is an Open Access article distributed under the terms of the Creative commons Attribution License (https://creativecommons.org/licenses/BY/4.0 (https://creativecommons.org/licenses/by/4.0/) ), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Articles Adegoke, Omolade O Ajao, Akinlabi E Ano-Edward, Gbemi H Congenital infantile digital fibromatosis: a case report and review of the literature |
title | Congenital infantile digital fibromatosis: a case report and review of the literature |
title_full | Congenital infantile digital fibromatosis: a case report and review of the literature |
title_fullStr | Congenital infantile digital fibromatosis: a case report and review of the literature |
title_full_unstemmed | Congenital infantile digital fibromatosis: a case report and review of the literature |
title_short | Congenital infantile digital fibromatosis: a case report and review of the literature |
title_sort | congenital infantile digital fibromatosis: a case report and review of the literature |
topic | Articles |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8351811/ https://www.ncbi.nlm.nih.gov/pubmed/34394250 http://dx.doi.org/10.4314/ahs.v20i4.42 |
work_keys_str_mv | AT adegokeomoladeo congenitalinfantiledigitalfibromatosisacasereportandreviewoftheliterature AT ajaoakinlabie congenitalinfantiledigitalfibromatosisacasereportandreviewoftheliterature AT anoedwardgbemih congenitalinfantiledigitalfibromatosisacasereportandreviewoftheliterature |