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Update on Diagnosis and Treatment of Adult Pulmonary Alveolar Proteinosis

Pulmonary alveolar proteinosis (PAP) is a rare pulmonary surfactant homeostasis disorder resulting in buildup of lipo-proteinaceous material within the alveoli. PAP is classified as primary (autoimmune and hereditary), secondary, congenital and unclassifiable type based on the underlying pathogenesi...

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Detalles Bibliográficos
Autores principales: Iftikhar, Hira, Nair, Girish B, Kumar, Anupam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8364424/
https://www.ncbi.nlm.nih.gov/pubmed/34408422
http://dx.doi.org/10.2147/TCRM.S193884