Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report

INTRODUCTION: Patients with Peutz-Jeghers syndrome (PJS) have high risk of malignancies, including gynecological cancers. Gastric type mucinous cervical adenocarcinoma might be presented in about 11–17% of PJS patients but the literature about this is limited. CASE PRESENTATION: We presented a rare...

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Detalles Bibliográficos
Autores principales: Vu Dinh, Giap, Doan Thi Hong, Nhat, Vo Ngoc, Tu, Nguyen Thanh, Long, Hoang Thi, Hoai, Phung Thi, Huyen
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8371195/
https://www.ncbi.nlm.nih.gov/pubmed/34429956
http://dx.doi.org/10.1016/j.amsu.2021.102700
Descripción
Sumario:INTRODUCTION: Patients with Peutz-Jeghers syndrome (PJS) have high risk of malignancies, including gynecological cancers. Gastric type mucinous cervical adenocarcinoma might be presented in about 11–17% of PJS patients but the literature about this is limited. CASE PRESENTATION: We presented a rare case of a 39-year-old Vietnamese woman with Peutz-Jeghers syndrome who has gastric type adenocarcinoma (GAS) of the cervix. She underwent radical hysterectomy, and the diagnosis was confirmed on final pathology. CONCLUSIONS: Oncologists and pathologists should recognize this rare clinical scenario for early diagnosis and treatment. This subtype also has an aggressive nature and poor prognosis.

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