Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report

INTRODUCTION: Patients with Peutz-Jeghers syndrome (PJS) have high risk of malignancies, including gynecological cancers. Gastric type mucinous cervical adenocarcinoma might be presented in about 11–17% of PJS patients but the literature about this is limited. CASE PRESENTATION: We presented a rare...

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Autores principales: Vu Dinh, Giap, Doan Thi Hong, Nhat, Vo Ngoc, Tu, Nguyen Thanh, Long, Hoang Thi, Hoai, Phung Thi, Huyen
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8371195/
https://www.ncbi.nlm.nih.gov/pubmed/34429956
http://dx.doi.org/10.1016/j.amsu.2021.102700
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author Vu Dinh, Giap
Doan Thi Hong, Nhat
Vo Ngoc, Tu
Nguyen Thanh, Long
Hoang Thi, Hoai
Phung Thi, Huyen
author_facet Vu Dinh, Giap
Doan Thi Hong, Nhat
Vo Ngoc, Tu
Nguyen Thanh, Long
Hoang Thi, Hoai
Phung Thi, Huyen
author_sort Vu Dinh, Giap
collection PubMed
description INTRODUCTION: Patients with Peutz-Jeghers syndrome (PJS) have high risk of malignancies, including gynecological cancers. Gastric type mucinous cervical adenocarcinoma might be presented in about 11–17% of PJS patients but the literature about this is limited. CASE PRESENTATION: We presented a rare case of a 39-year-old Vietnamese woman with Peutz-Jeghers syndrome who has gastric type adenocarcinoma (GAS) of the cervix. She underwent radical hysterectomy, and the diagnosis was confirmed on final pathology. CONCLUSIONS: Oncologists and pathologists should recognize this rare clinical scenario for early diagnosis and treatment. This subtype also has an aggressive nature and poor prognosis.
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spelling pubmed-83711952021-08-23 Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report Vu Dinh, Giap Doan Thi Hong, Nhat Vo Ngoc, Tu Nguyen Thanh, Long Hoang Thi, Hoai Phung Thi, Huyen Ann Med Surg (Lond) Case Report INTRODUCTION: Patients with Peutz-Jeghers syndrome (PJS) have high risk of malignancies, including gynecological cancers. Gastric type mucinous cervical adenocarcinoma might be presented in about 11–17% of PJS patients but the literature about this is limited. CASE PRESENTATION: We presented a rare case of a 39-year-old Vietnamese woman with Peutz-Jeghers syndrome who has gastric type adenocarcinoma (GAS) of the cervix. She underwent radical hysterectomy, and the diagnosis was confirmed on final pathology. CONCLUSIONS: Oncologists and pathologists should recognize this rare clinical scenario for early diagnosis and treatment. This subtype also has an aggressive nature and poor prognosis. Elsevier 2021-08-10 /pmc/articles/PMC8371195/ /pubmed/34429956 http://dx.doi.org/10.1016/j.amsu.2021.102700 Text en © 2021 The Authors https://creativecommons.org/licenses/by/4.0/This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Vu Dinh, Giap
Doan Thi Hong, Nhat
Vo Ngoc, Tu
Nguyen Thanh, Long
Hoang Thi, Hoai
Phung Thi, Huyen
Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report
title Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report
title_full Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report
title_fullStr Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report
title_full_unstemmed Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report
title_short Peuzt – Jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: A case report
title_sort peuzt – jeghers syndrome with gastric type mucinous endocervical adenocarcinoma in a young woman: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8371195/
https://www.ncbi.nlm.nih.gov/pubmed/34429956
http://dx.doi.org/10.1016/j.amsu.2021.102700
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