Primary Immune Regulatory Disorders With an Autoimmune Lymphoproliferative Syndrome-Like Phenotype: Immunologic Evaluation, Early Diagnosis and Management

Primary immune regulatory disorders (PIRD) are associated with autoimmunity, autoinflammation and/or dysregulation of lymphocyte homeostasis. Autoimmune lymphoproliferative syndrome (ALPS) is a PIRD due to an apoptotic defect in Fas-FasL pathway and characterized by benign and chronic lymphoprolifer...

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Detalles Bibliográficos
Autores principales: López-Nevado, Marta, González-Granado, Luis I., Ruiz-García, Raquel, Pleguezuelo, Daniel, Cabrera-Marante, Oscar, Salmón, Nerea, Blanco-Lobo, Pilar, Domínguez-Pinilla, Nerea, Rodríguez-Pena, Rebeca, Sebastián, Elena, Cruz-Rojo, Jaime, Olbrich, Peter, Ruiz-Contreras, Jesús, Paz-Artal, Estela, Neth, Olaf, Allende, Luis M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2021
Materias:
Immunology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8382720/
https://www.ncbi.nlm.nih.gov/pubmed/34447369
http://dx.doi.org/10.3389/fimmu.2021.671755

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8382720/
https://www.ncbi.nlm.nih.gov/pubmed/34447369
http://dx.doi.org/10.3389/fimmu.2021.671755

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