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Primary Immune Regulatory Disorders With an Autoimmune Lymphoproliferative Syndrome-Like Phenotype: Immunologic Evaluation, Early Diagnosis and Management
Primary immune regulatory disorders (PIRD) are associated with autoimmunity, autoinflammation and/or dysregulation of lymphocyte homeostasis. Autoimmune lymphoproliferative syndrome (ALPS) is a PIRD due to an apoptotic defect in Fas-FasL pathway and characterized by benign and chronic lymphoprolifer...
Autores principales: | López-Nevado, Marta, González-Granado, Luis I., Ruiz-García, Raquel, Pleguezuelo, Daniel, Cabrera-Marante, Oscar, Salmón, Nerea, Blanco-Lobo, Pilar, Domínguez-Pinilla, Nerea, Rodríguez-Pena, Rebeca, Sebastián, Elena, Cruz-Rojo, Jaime, Olbrich, Peter, Ruiz-Contreras, Jesús, Paz-Artal, Estela, Neth, Olaf, Allende, Luis M. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8382720/ https://www.ncbi.nlm.nih.gov/pubmed/34447369 http://dx.doi.org/10.3389/fimmu.2021.671755 |
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