Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E

Elexacaftor/tezacaftor/ivacaftor (ETI) is a cystic fibrosis (CF) transmembrane regulator (CFTR) modulator. It is known to be efficacious in stable patients with severe pneumopathy, but there are few data concerning its effectiveness during acute exacerbations. We here describe its use in a woman wit...

Descripción completa

Detalles Bibliográficos
Autores principales: Salvatore, Donatello, Colangelo, Carmela, D’Andria, Michele, Marsicovetere, Giovanni, Passarella, Domenica
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8385458/
https://www.ncbi.nlm.nih.gov/pubmed/34466263
http://dx.doi.org/10.1002/ccr3.4713
_version_ 1783742097128423424
author Salvatore, Donatello
Colangelo, Carmela
D’Andria, Michele
Marsicovetere, Giovanni
Passarella, Domenica
author_facet Salvatore, Donatello
Colangelo, Carmela
D’Andria, Michele
Marsicovetere, Giovanni
Passarella, Domenica
author_sort Salvatore, Donatello
collection PubMed
description Elexacaftor/tezacaftor/ivacaftor (ETI) is a cystic fibrosis (CF) transmembrane regulator (CFTR) modulator. It is known to be efficacious in stable patients with severe pneumopathy, but there are few data concerning its effectiveness during acute exacerbations. We here describe its use in a woman with CF and respiratory failure.
format Online
Article
Text
id pubmed-8385458
institution National Center for Biotechnology Information
language English
publishDate 2021
publisher John Wiley and Sons Inc.
record_format MEDLINE/PubMed
spelling pubmed-83854582021-08-30 Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E Salvatore, Donatello Colangelo, Carmela D’Andria, Michele Marsicovetere, Giovanni Passarella, Domenica Clin Case Rep Case Report Elexacaftor/tezacaftor/ivacaftor (ETI) is a cystic fibrosis (CF) transmembrane regulator (CFTR) modulator. It is known to be efficacious in stable patients with severe pneumopathy, but there are few data concerning its effectiveness during acute exacerbations. We here describe its use in a woman with CF and respiratory failure. John Wiley and Sons Inc. 2021-08-25 /pmc/articles/PMC8385458/ /pubmed/34466263 http://dx.doi.org/10.1002/ccr3.4713 Text en © 2021 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Report
Salvatore, Donatello
Colangelo, Carmela
D’Andria, Michele
Marsicovetere, Giovanni
Passarella, Domenica
Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E
title Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E
title_full Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E
title_fullStr Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E
title_full_unstemmed Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E
title_short Elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype F508DEL/G1244E
title_sort elexacaftor/tezacaftor/ivacaftor as rescue therapy in a patient with the cystic fibrosis genotype f508del/g1244e
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8385458/
https://www.ncbi.nlm.nih.gov/pubmed/34466263
http://dx.doi.org/10.1002/ccr3.4713
work_keys_str_mv AT salvatoredonatello elexacaftortezacaftorivacaftorasrescuetherapyinapatientwiththecysticfibrosisgenotypef508delg1244e
AT colangelocarmela elexacaftortezacaftorivacaftorasrescuetherapyinapatientwiththecysticfibrosisgenotypef508delg1244e
AT dandriamichele elexacaftortezacaftorivacaftorasrescuetherapyinapatientwiththecysticfibrosisgenotypef508delg1244e
AT marsicoveteregiovanni elexacaftortezacaftorivacaftorasrescuetherapyinapatientwiththecysticfibrosisgenotypef508delg1244e
AT passarelladomenica elexacaftortezacaftorivacaftorasrescuetherapyinapatientwiththecysticfibrosisgenotypef508delg1244e

Ejemplares similares