Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications

Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are n...

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Autores principales: Misra, Satyajeet, Mohanty, Satyapriya, Sathia, Siddhartha, Mahapatra, Rudra Pratap, Tapuria, Priyank
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8404579/
https://www.ncbi.nlm.nih.gov/pubmed/34269268
http://dx.doi.org/10.4103/aca.ACA_198_20
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author Misra, Satyajeet
Mohanty, Satyapriya
Sathia, Siddhartha
Mahapatra, Rudra Pratap
Tapuria, Priyank
author_facet Misra, Satyajeet
Mohanty, Satyapriya
Sathia, Siddhartha
Mahapatra, Rudra Pratap
Tapuria, Priyank
author_sort Misra, Satyajeet
collection PubMed
description Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are no previous reports of absent right superior vena cava (SVC) in children with Holt-Oram syndrome. We present images of a case where the diagnosis of absent right SVC with persistent left SVC was made with intraoperative transesophageal echocardiography and discuss the anesthetic and perfusion implications of such findings.
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spelling pubmed-84045792021-09-07 Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications Misra, Satyajeet Mohanty, Satyapriya Sathia, Siddhartha Mahapatra, Rudra Pratap Tapuria, Priyank Ann Card Anaesth Interesting Image Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are no previous reports of absent right superior vena cava (SVC) in children with Holt-Oram syndrome. We present images of a case where the diagnosis of absent right SVC with persistent left SVC was made with intraoperative transesophageal echocardiography and discuss the anesthetic and perfusion implications of such findings. Wolters Kluwer - Medknow 2021 2021-07-09 /pmc/articles/PMC8404579/ /pubmed/34269268 http://dx.doi.org/10.4103/aca.ACA_198_20 Text en Copyright: © 2021 Annals of Cardiac Anaesthesia https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Interesting Image
Misra, Satyajeet
Mohanty, Satyapriya
Sathia, Siddhartha
Mahapatra, Rudra Pratap
Tapuria, Priyank
Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
title Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
title_full Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
title_fullStr Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
title_full_unstemmed Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
title_short Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
title_sort diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with holt-oram syndrome: anesthetic and perfusion implications
topic Interesting Image
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8404579/
https://www.ncbi.nlm.nih.gov/pubmed/34269268
http://dx.doi.org/10.4103/aca.ACA_198_20
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