Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications
Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are n...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Wolters Kluwer - Medknow
2021
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8404579/ https://www.ncbi.nlm.nih.gov/pubmed/34269268 http://dx.doi.org/10.4103/aca.ACA_198_20 |
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author | Misra, Satyajeet Mohanty, Satyapriya Sathia, Siddhartha Mahapatra, Rudra Pratap Tapuria, Priyank |
author_facet | Misra, Satyajeet Mohanty, Satyapriya Sathia, Siddhartha Mahapatra, Rudra Pratap Tapuria, Priyank |
author_sort | Misra, Satyajeet |
collection | PubMed |
description | Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are no previous reports of absent right superior vena cava (SVC) in children with Holt-Oram syndrome. We present images of a case where the diagnosis of absent right SVC with persistent left SVC was made with intraoperative transesophageal echocardiography and discuss the anesthetic and perfusion implications of such findings. |
format | Online Article Text |
id | pubmed-8404579 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Wolters Kluwer - Medknow |
record_format | MEDLINE/PubMed |
spelling | pubmed-84045792021-09-07 Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications Misra, Satyajeet Mohanty, Satyapriya Sathia, Siddhartha Mahapatra, Rudra Pratap Tapuria, Priyank Ann Card Anaesth Interesting Image Holt-Oram syndrome is a rare autosomal disorder with cardiac, vascular, and upper limb anomalies. Previous reports have described anesthetic and perioperative challenges including difficulty in arterial and venous cannulations, airway management and rhythm, and temperature abnormalities. There are no previous reports of absent right superior vena cava (SVC) in children with Holt-Oram syndrome. We present images of a case where the diagnosis of absent right SVC with persistent left SVC was made with intraoperative transesophageal echocardiography and discuss the anesthetic and perfusion implications of such findings. Wolters Kluwer - Medknow 2021 2021-07-09 /pmc/articles/PMC8404579/ /pubmed/34269268 http://dx.doi.org/10.4103/aca.ACA_198_20 Text en Copyright: © 2021 Annals of Cardiac Anaesthesia https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Interesting Image Misra, Satyajeet Mohanty, Satyapriya Sathia, Siddhartha Mahapatra, Rudra Pratap Tapuria, Priyank Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications |
title | Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications |
title_full | Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications |
title_fullStr | Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications |
title_full_unstemmed | Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications |
title_short | Diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with Holt-Oram syndrome: Anesthetic and perfusion implications |
title_sort | diagnosis of absent right superior vena cava with intraoperative transesophageal echocardiography in a child with holt-oram syndrome: anesthetic and perfusion implications |
topic | Interesting Image |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8404579/ https://www.ncbi.nlm.nih.gov/pubmed/34269268 http://dx.doi.org/10.4103/aca.ACA_198_20 |
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