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Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report

Miyoshi myopathy (MM) is a rare autosomal recessive disorder caused by dysferlin (DYSF) gene mutation. Miyoshi myopathy-inducing mutation sites in the DYSF gene have been discovered worldwide. In the present study, a patient with progressive lower extremity weakness is reported, for which MM was dia...

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Autores principales: Yan, Hai-Yan, Xie, Ya-Nan, Han, Jing-Zhe, Song, Xue-Qin
Formato: Online Artículo Texto
Lenguaje:English
Publicado: International Society of Musculoskeletal and Neuronal Interactions 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8426653/
https://www.ncbi.nlm.nih.gov/pubmed/34465679
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author Yan, Hai-Yan
Xie, Ya-Nan
Han, Jing-Zhe
Song, Xue-Qin
author_facet Yan, Hai-Yan
Xie, Ya-Nan
Han, Jing-Zhe
Song, Xue-Qin
author_sort Yan, Hai-Yan
collection PubMed
description Miyoshi myopathy (MM) is a rare autosomal recessive disorder caused by dysferlin (DYSF) gene mutation. Miyoshi myopathy-inducing mutation sites in the DYSF gene have been discovered worldwide. In the present study, a patient with progressive lower extremity weakness is reported, for which MM was diagnosed according to clinical manifestations, muscle biopsy, and immunohistochemistry. In addition, the DYSF gene of the patient and his parents was sequenced and analyzed and two heterozygous mutations of the DYSF gene (c.4756C> T and c.5316dupC) were discovered. The first mutation correlated with MM while the second was a new mutation. The patient was diagnosed with a compound heterozygous mutation. The mutation site is a new member of pathogenic MM gene mutations.
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spelling pubmed-84266532021-09-13 Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report Yan, Hai-Yan Xie, Ya-Nan Han, Jing-Zhe Song, Xue-Qin J Musculoskelet Neuronal Interact Case Report Miyoshi myopathy (MM) is a rare autosomal recessive disorder caused by dysferlin (DYSF) gene mutation. Miyoshi myopathy-inducing mutation sites in the DYSF gene have been discovered worldwide. In the present study, a patient with progressive lower extremity weakness is reported, for which MM was diagnosed according to clinical manifestations, muscle biopsy, and immunohistochemistry. In addition, the DYSF gene of the patient and his parents was sequenced and analyzed and two heterozygous mutations of the DYSF gene (c.4756C> T and c.5316dupC) were discovered. The first mutation correlated with MM while the second was a new mutation. The patient was diagnosed with a compound heterozygous mutation. The mutation site is a new member of pathogenic MM gene mutations. International Society of Musculoskeletal and Neuronal Interactions 2021 /pmc/articles/PMC8426653/ /pubmed/34465679 Text en Copyright: © Journal of Musculoskeletal and Neuronal Interactions https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 4.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Yan, Hai-Yan
Xie, Ya-Nan
Han, Jing-Zhe
Song, Xue-Qin
Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report
title Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report
title_full Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report
title_fullStr Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report
title_full_unstemmed Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report
title_short Mutation at a new allele of the dysferlin gene causes Miyoshi myopathy: A case report
title_sort mutation at a new allele of the dysferlin gene causes miyoshi myopathy: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8426653/
https://www.ncbi.nlm.nih.gov/pubmed/34465679
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