Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed

Neuroblastic tumors (NTs) include neuroblastoma, ganglioneuroblastoma, and ganglioneuroma (GN). They are very rare in adults. The Surveillance, Epidemiology, and End Results identified 144 patients ≥20 years old at diagnosis (6.1%) from 1973 to 2002. GNs account for 14% of all localized NT. Since 19...

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Autores principales: Dhali, Arkadeep, Ray, Sukanta, Dhali, Gopal Krishna, Ghosh, Ranajoy, Sarkar, Avik
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Medical Publishers, Inc. 2021
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8440055/
https://www.ncbi.nlm.nih.gov/pubmed/34541318
http://dx.doi.org/10.1055/s-0041-1735644
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author Dhali, Arkadeep
Ray, Sukanta
Dhali, Gopal Krishna
Ghosh, Ranajoy
Sarkar, Avik
author_facet Dhali, Arkadeep
Ray, Sukanta
Dhali, Gopal Krishna
Ghosh, Ranajoy
Sarkar, Avik
author_sort Dhali, Arkadeep
collection PubMed
description Neuroblastic tumors (NTs) include neuroblastoma, ganglioneuroblastoma, and ganglioneuroma (GN). They are very rare in adults. The Surveillance, Epidemiology, and End Results identified 144 patients ≥20 years old at diagnosis (6.1%) from 1973 to 2002. GNs account for 14% of all localized NT. Since 1957, a total of four cases of GN of the duodenum have been reported. We report a novel case of GN of the periampullary region in the duodenum in a 41-year-old man presenting with chronic upper gastrointestinal bleed. Given the rarity of GNs in this age group and the nonspecificity of radiological features, this diagnosis is often missed until histopathology is done. This may negatively affect the prognosis of an otherwise well-prognosticated disease.
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spelling pubmed-84400552021-09-16 Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed Dhali, Arkadeep Ray, Sukanta Dhali, Gopal Krishna Ghosh, Ranajoy Sarkar, Avik Surg J (N Y) Neuroblastic tumors (NTs) include neuroblastoma, ganglioneuroblastoma, and ganglioneuroma (GN). They are very rare in adults. The Surveillance, Epidemiology, and End Results identified 144 patients ≥20 years old at diagnosis (6.1%) from 1973 to 2002. GNs account for 14% of all localized NT. Since 1957, a total of four cases of GN of the duodenum have been reported. We report a novel case of GN of the periampullary region in the duodenum in a 41-year-old man presenting with chronic upper gastrointestinal bleed. Given the rarity of GNs in this age group and the nonspecificity of radiological features, this diagnosis is often missed until histopathology is done. This may negatively affect the prognosis of an otherwise well-prognosticated disease. Thieme Medical Publishers, Inc. 2021-09-14 /pmc/articles/PMC8440055/ /pubmed/34541318 http://dx.doi.org/10.1055/s-0041-1735644 Text en The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. ( https://creativecommons.org/licenses/by/4.0/ ) https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Dhali, Arkadeep
Ray, Sukanta
Dhali, Gopal Krishna
Ghosh, Ranajoy
Sarkar, Avik
Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed
title Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed
title_full Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed
title_fullStr Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed
title_full_unstemmed Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed
title_short Duodenal Ganglioneuroma: A Rare Tumor Causing Upper Gastrointestinal Bleed
title_sort duodenal ganglioneuroma: a rare tumor causing upper gastrointestinal bleed
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8440055/
https://www.ncbi.nlm.nih.gov/pubmed/34541318
http://dx.doi.org/10.1055/s-0041-1735644
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AT ghoshranajoy duodenalganglioneuromaararetumorcausinguppergastrointestinalbleed
AT sarkaravik duodenalganglioneuromaararetumorcausinguppergastrointestinalbleed

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