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Dystrophin Dp71 Subisoforms Localize to the Mitochondria of Human Cells

Duchenne muscular dystrophy (DMD) is a fatal muscle wasting disease caused by deficiency in dystrophin, a protein product encoded by the DMD gene. Mitochondrial dysfunction is now attracting much attention as a central player in DMD pathology. However, dystrophin has never been explored in human mit...

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Detalles Bibliográficos
Autores principales:	Niba, Emma Tabe Eko, Awano, Hiroyuki, Lee, Tomoko, Takeshima, Yasuhiro, Shinohara, Masakazu, Nishio, Hisahide, Matsuo, Masafumi
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8468555/ https://www.ncbi.nlm.nih.gov/pubmed/34575126 http://dx.doi.org/10.3390/life11090978

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