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Current and Future Treatments in Primary Ciliary Dyskinesia

Primary ciliary dyskinesia (PCD) is a rare genetic ciliopathy in which mucociliary clearance is disturbed by the abnormal motion of cilia or there is a severe reduction in the generation of multiple motile cilia. Lung damage ensues due to recurrent airway infections, sometimes even resulting in resp...

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Detalles Bibliográficos
Autores principales:	Paff, Tamara, Omran, Heymut, Nielsen, Kim G., Haarman, Eric G.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8470068/ https://www.ncbi.nlm.nih.gov/pubmed/34575997 http://dx.doi.org/10.3390/ijms22189834

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