Cargando…

The Impact of Highly Effective CFTR Modulators on Growth and Nutrition Status

Patients with cystic fibrosis (CF) are at increased risk of malnutrition and growth failure due to multiple factors as a result of suboptimal or absent function of the CFTR chloride channel protein. Dysfunctional CFTR contributes to increased energy expenditure, exocrine pancreatic insufficiency cau...

Descripción completa

Detalles Bibliográficos
Autores principales:	Bass, Rosara, Brownell, Jefferson N., Stallings, Virginia A.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8470943/ https://www.ncbi.nlm.nih.gov/pubmed/34578785 http://dx.doi.org/10.3390/nu13092907

Ejemplares similares

Bone accrual and structural changes over one year in youth with cystic fibrosis
por: Bass, Rosara M., et al.
Publicado: (2022)

Nutritional impact of CFTR modulators in children with cystic fibrosis
por: Gaschignard, Margaux, et al.
Publicado: (2023)

CFTR Modulator Therapies: Potential Impact on Airway Infections in Cystic Fibrosis
por: Saluzzo, Francesca, et al.
Publicado: (2022)

Impact of Airway Inflammation on the Efficacy of CFTR Modulators
por: Ribeiro, Carla M. P., et al.
Publicado: (2021)

Role of inhaled antibiotics in the era of highly effective CFTR modulators
por: Elborn, J. Stuart, et al.
Publicado: (2023)

Management of Individual Patient Expectations When Starting with Highly Effective CFTR Modulators
por: Aalbers, Bente L., et al.
Publicado: (2021)

The Effect of CFTR Modulators on Airway Infection in Cystic Fibrosis
por: Harvey, Caitlyn, et al.
Publicado: (2022)

Utilization of the Healthy Eating Index in Cystic Fibrosis
por: Bass, Rosara Milstein, et al.
Publicado: (2022)

CFTR Modulator Therapy and Its Impact on Lung Transplantation in Cystic Fibrosis
por: Benden, Christian, et al.
Publicado: (2021)

CFTR Modulators: Impact on Fertility, Pregnancy, and Lactation in Women with Cystic Fibrosis
por: Taylor-Cousar, Jennifer L.
Publicado: (2020)

Real-life impact of highly effective CFTR modulator therapy in children with cystic fibrosis
por: Olivier, Margarete, et al.
Publicado: (2023)

Two Patients with Fulminant Clostridium difficile Enteritis Who Had Not Undergone Total Colectomy: A Case Series and Review of the Literature
por: Beal, Eliza W., et al.
Publicado: (2015)

Impact of CFTR Modulators on the Impaired Function of Phagocytes in Cystic Fibrosis Lung Disease
por: Meoli, Aniello, et al.
Publicado: (2022)

CF Fungal Disease in the Age of CFTR Modulators
por: Bercusson, Amelia, et al.
Publicado: (2021)

Nutritional Status and Circulating Levels of Fat-Soluble Vitamins in Cystic Fibrosis Patients: A Cohort Study and Evaluation of the Effect of CFTR Modulators
por: Francalanci, Michela, et al.
Publicado: (2023)

Pharmacological Responses of the G542X-CFTR to CFTR Modulators
por: Fang, Xinxiu, et al.
Publicado: (2022)

Clinical Consequences and Functional Impact of the Rare S737F CFTR Variant and Its Responsiveness to CFTR Modulators
por: Terlizzi, Vito, et al.
Publicado: (2023)

Rapid therapeutic advances in CFTR modulator science
por: Clancy, John P.
Publicado: (2018)

Impact of CFTR modulator use on outcomes in people with severe cystic fibrosis lung disease
por: Shteinberg, Michal, et al.
Publicado: (2020)

CFTR Modulators: Does One Dose Fit All?
por: van der Meer, Renske, et al.
Publicado: (2021)

Airway Inflammation and Host Responses in the Era of CFTR Modulators
por: Keown, Karen, et al.
Publicado: (2020)

Regulation of CFTR Biogenesis by the Proteostatic Network and Pharmacological Modulators
por: Estabrooks, Samuel, et al.
Publicado: (2020)

Islet-intrinsic effects of CFTR mutation
por: Koivula, Fiona N. Manderson, et al.
Publicado: (2016)

The PROSPECT Is Bright for CFTR Modulators
por: Montemayor, Kristina, et al.
Publicado: (2021)

Of muscle modulation and the CFTR gate
por: Adler, Elizabeth M.
Publicado: (2015)

Impact of CFTR modulation with Ivacaftor on Gut Microbiota and Intestinal Inflammation
por: Ooi, Chee Y., et al.
Publicado: (2018)

Triplet CFTR modulators: future prospects for treatment of cystic fibrosis
por: Chaudary, Nauman
Publicado: (2018)

Airway Epithelial Inflammation In Vitro Augments the Rescue of Mutant CFTR by Current CFTR Modulator Therapies
por: Gentzsch, Martina, et al.
Publicado: (2021)

Vitamin D status, nutrition and growth in HIV-infected mothers and HIV-exposed infants and children in Botswana
por: Tindall, Alyssa M., et al.
Publicado: (2020)

The effect of CFTR modulators on structural lung disease in cystic fibrosis
por: Mok, L. Clara, et al.
Publicado: (2023)

Modulation of CFTR gating by permeant ions
por: Yeh, Han-I, et al.
Publicado: (2015)

Therapeutic Approaches for Patients with Cystic Fibrosis Not Eligible for Current CFTR Modulators
por: Fajac, Isabelle, et al.
Publicado: (2021)

Fertility, Pregnancy and Lactation Considerations for Women with CF in the CFTR Modulator Era
por: Jain, Raksha, et al.
Publicado: (2021)

Advancing clinical development pathways for new CFTR modulators in cystic fibrosis
por: Mayer-Hamblett, Nicole, et al.
Publicado: (2016)

CFTR Modulators in People with Cystic Fibrosis: Real-World Evidence in France
por: Regard, Lucile, et al.
Publicado: (2022)

Progress in precision medicine in cystic fibrosis: a focus on CFTR modulator therapy
por: Tewkesbury, Daniel H., et al.
Publicado: (2021)

The Role of MMPs in the Era of CFTR Modulators: An Additional Target for Cystic Fibrosis Patients?
por: Esposito, Renata, et al.
Publicado: (2023)

Revisiting Host-Pathogen Interactions in Cystic Fibrosis Lungs in the Era of CFTR Modulators
por: Ribeiro, Carla M. P., et al.
Publicado: (2023)

CFTR modulators: transformative therapies for cystic fibrosis
por: Dwight, Mary, et al.
Publicado: (2021)

State-dependent modulation of CFTR gating by pyrophosphate
por: Tsai, Ming-Feng, et al.
Publicado: (2009)

Cannot write session to /tmp/vufind_sessions/sess_4dmidu1i78o0cb29c52dvk4sa9