Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis

We report on an 11-year-old girl with cystic fibrosis who presented with thoracic pain and an extensive subcutaneous emphysema and subsequently developed progressive respiratory distress. The chest computed tomography revealed a huge pneumomediastinum. Due to the development of severe respiratory fa...

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Autores principales: Zsiborás, Csaba, Adonyi, Mária, Stankovics, József, Farkas, András, Vajda, Peter, Rózsai, Barnabás
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Georg Thieme Verlag KG 2021
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8486495/
https://www.ncbi.nlm.nih.gov/pubmed/34616649
http://dx.doi.org/10.1055/s-0041-1731274
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author Zsiborás, Csaba
Adonyi, Mária
Stankovics, József
Farkas, András
Vajda, Peter
Rózsai, Barnabás
author_facet Zsiborás, Csaba
Adonyi, Mária
Stankovics, József
Farkas, András
Vajda, Peter
Rózsai, Barnabás
author_sort Zsiborás, Csaba
collection PubMed
description We report on an 11-year-old girl with cystic fibrosis who presented with thoracic pain and an extensive subcutaneous emphysema and subsequently developed progressive respiratory distress. The chest computed tomography revealed a huge pneumomediastinum. Due to the development of severe respiratory failure, urgent needle thoracocentesis was necessary that resulted in only temporary improvement. Therefore, under general anesthesia two mediastinal drains were introduced. Using active suction, the size of the pneumomediastinum decreased gradually and the drains were removed after 3 weeks. Here, we describe an extremely rare situation, when acute surgical intervention was necessary in a child with spontaneous pneumomediastinum.
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spelling pubmed-84864952021-10-05 Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis Zsiborás, Csaba Adonyi, Mária Stankovics, József Farkas, András Vajda, Peter Rózsai, Barnabás European J Pediatr Surg Rep We report on an 11-year-old girl with cystic fibrosis who presented with thoracic pain and an extensive subcutaneous emphysema and subsequently developed progressive respiratory distress. The chest computed tomography revealed a huge pneumomediastinum. Due to the development of severe respiratory failure, urgent needle thoracocentesis was necessary that resulted in only temporary improvement. Therefore, under general anesthesia two mediastinal drains were introduced. Using active suction, the size of the pneumomediastinum decreased gradually and the drains were removed after 3 weeks. Here, we describe an extremely rare situation, when acute surgical intervention was necessary in a child with spontaneous pneumomediastinum. Georg Thieme Verlag KG 2021-10-01 /pmc/articles/PMC8486495/ /pubmed/34616649 http://dx.doi.org/10.1055/s-0041-1731274 Text en The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. ( https://creativecommons.org/licenses/by/4.0/ ) https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Zsiborás, Csaba
Adonyi, Mária
Stankovics, József
Farkas, András
Vajda, Peter
Rózsai, Barnabás
Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis
title Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis
title_full Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis
title_fullStr Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis
title_full_unstemmed Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis
title_short Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis
title_sort severe spontaneous pneumomediastinum in a girl with cystic fibrosis
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8486495/
https://www.ncbi.nlm.nih.gov/pubmed/34616649
http://dx.doi.org/10.1055/s-0041-1731274
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