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Plexiform neurofibroma with nevus of ota-rare presentation
Plexiform neurofibroma (PNF) is a rare form of neurofibromatosis type 1 which is rarely seen isolated. This generally spreads along the peripheral nerve and may affect some nervous rami. This is a poorly circumscribed and locally invasive tumor. About 21% of patients with NF-I are affected with PNFs...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Medknow Publications & Media Pvt Ltd
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8491357/ https://www.ncbi.nlm.nih.gov/pubmed/34703146 http://dx.doi.org/10.4103/0973-029X.325263 |
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author | Taneja, Lavina Dokwal, Sushil Kumar Prajapat, Jyoti Arya, Vishal |
author_facet | Taneja, Lavina Dokwal, Sushil Kumar Prajapat, Jyoti Arya, Vishal |
author_sort | Taneja, Lavina |
collection | PubMed |
description | Plexiform neurofibroma (PNF) is a rare form of neurofibromatosis type 1 which is rarely seen isolated. This generally spreads along the peripheral nerve and may affect some nervous rami. This is a poorly circumscribed and locally invasive tumor. About 21% of patients with NF-I are affected with PNFs. The nevus of Ota also called oculodermal melanocytosis is a macular discoloration of the face. It is most commonly found in the Japanese and very rare in the Indian subcontinent. It is unilateral oculodermal melanosis along the first two branches of the trigeminal nerve. We hereby present a very rare case of occurrence of isolated PNF (not associated with neurofibromatosis type 1) along with nevus of ota of the left side of the face in a 28-year-old female with thorough radiographic work up. |
format | Online Article Text |
id | pubmed-8491357 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-84913572021-10-25 Plexiform neurofibroma with nevus of ota-rare presentation Taneja, Lavina Dokwal, Sushil Kumar Prajapat, Jyoti Arya, Vishal J Oral Maxillofac Pathol Case Report Plexiform neurofibroma (PNF) is a rare form of neurofibromatosis type 1 which is rarely seen isolated. This generally spreads along the peripheral nerve and may affect some nervous rami. This is a poorly circumscribed and locally invasive tumor. About 21% of patients with NF-I are affected with PNFs. The nevus of Ota also called oculodermal melanocytosis is a macular discoloration of the face. It is most commonly found in the Japanese and very rare in the Indian subcontinent. It is unilateral oculodermal melanosis along the first two branches of the trigeminal nerve. We hereby present a very rare case of occurrence of isolated PNF (not associated with neurofibromatosis type 1) along with nevus of ota of the left side of the face in a 28-year-old female with thorough radiographic work up. Medknow Publications & Media Pvt Ltd 2021 2021-08-31 /pmc/articles/PMC8491357/ /pubmed/34703146 http://dx.doi.org/10.4103/0973-029X.325263 Text en Copyright: © 2021 Journal of Oral and Maxillofacial Pathology https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Taneja, Lavina Dokwal, Sushil Kumar Prajapat, Jyoti Arya, Vishal Plexiform neurofibroma with nevus of ota-rare presentation |
title | Plexiform neurofibroma with nevus of ota-rare presentation |
title_full | Plexiform neurofibroma with nevus of ota-rare presentation |
title_fullStr | Plexiform neurofibroma with nevus of ota-rare presentation |
title_full_unstemmed | Plexiform neurofibroma with nevus of ota-rare presentation |
title_short | Plexiform neurofibroma with nevus of ota-rare presentation |
title_sort | plexiform neurofibroma with nevus of ota-rare presentation |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8491357/ https://www.ncbi.nlm.nih.gov/pubmed/34703146 http://dx.doi.org/10.4103/0973-029X.325263 |
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