The Extent of Inflammatory Cell Infiltrate and Fibrosis in Lungs of Telomere- and Surfactant-Related Familial Pulmonary Fibrosis

Familial pulmonary fibrosis (FPF) is a monogenic disease most commonly involving telomere- (TERT) or surfactant- (SFTP) related mutations. These mutations have been shown to alter lymphocytic inflammatory responses, and FPF biopsies with histological lymphocytic infiltrates have been reported. Recen...

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Detalles Bibliográficos
Autores principales: van Batenburg, Aernoud A., van Oosterhout, Matthijs F. M., Knoppert, Sebastiaan N., Kazemier, Karin M., van der Vis, Joanne J., Grutters, Jan C., Goldschmeding, Roel, van Moorsel, Coline H. M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2021
Materias:
Medicine
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8497799/
https://www.ncbi.nlm.nih.gov/pubmed/34631753
http://dx.doi.org/10.3389/fmed.2021.736485

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