Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)

Sternal agenesis as well as ectopia cordis are extremely rare congenital malformations. We here report a single case treated in the Department of Paediatric Surgery in Benin. The study involved a 3-year-old girl with congenital sternal agenesis associated with ectopia cordis; firstly, she underwent...

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Autores principales: Gbenou, Antoine Séraphin, Bata, Abdel-Kémal Bori, Akodjènou, Joseph, Zoumènou, Eugène, Fiogbe, Armand Michel, Tristan, Jose Uroz
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8498673/
https://www.ncbi.nlm.nih.gov/pubmed/34659606
http://dx.doi.org/10.11604/pamj.2021.39.233.25646
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author Gbenou, Antoine Séraphin
Bata, Abdel-Kémal Bori
Akodjènou, Joseph
Zoumènou, Eugène
Fiogbe, Armand Michel
Tristan, Jose Uroz
author_facet Gbenou, Antoine Séraphin
Bata, Abdel-Kémal Bori
Akodjènou, Joseph
Zoumènou, Eugène
Fiogbe, Armand Michel
Tristan, Jose Uroz
author_sort Gbenou, Antoine Séraphin
collection PubMed
description Sternal agenesis as well as ectopia cordis are extremely rare congenital malformations. We here report a single case treated in the Department of Paediatric Surgery in Benin. The study involved a 3-year-old girl with congenital sternal agenesis associated with ectopia cordis; firstly, she underwent controlled healing. Then thoracoplasty was performed with favourable outcome. Long-term results are good. Now, she is 13 years old, is attending school and has a satisfactory clinical condition. This is one of the few cases reported in the literature. Optimal therapeutic management has been keeping the patient alive in West Africa.
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spelling pubmed-84986732021-10-15 Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin) Gbenou, Antoine Séraphin Bata, Abdel-Kémal Bori Akodjènou, Joseph Zoumènou, Eugène Fiogbe, Armand Michel Tristan, Jose Uroz Pan Afr Med J Case Report Sternal agenesis as well as ectopia cordis are extremely rare congenital malformations. We here report a single case treated in the Department of Paediatric Surgery in Benin. The study involved a 3-year-old girl with congenital sternal agenesis associated with ectopia cordis; firstly, she underwent controlled healing. Then thoracoplasty was performed with favourable outcome. Long-term results are good. Now, she is 13 years old, is attending school and has a satisfactory clinical condition. This is one of the few cases reported in the literature. Optimal therapeutic management has been keeping the patient alive in West Africa. The African Field Epidemiology Network 2021-08-11 /pmc/articles/PMC8498673/ /pubmed/34659606 http://dx.doi.org/10.11604/pamj.2021.39.233.25646 Text en Copyright: Antoine Séraphin Gbenou et al. https://creativecommons.org/licenses/by/4.0/The Pan African Medical Journal (ISSN: 1937-8688). This is an Open Access article distributed under the terms of the Creative Commons Attribution International 4.0 License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Gbenou, Antoine Séraphin
Bata, Abdel-Kémal Bori
Akodjènou, Joseph
Zoumènou, Eugène
Fiogbe, Armand Michel
Tristan, Jose Uroz
Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)
title Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)
title_full Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)
title_fullStr Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)
title_full_unstemmed Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)
title_short Agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au Bénin)
title_sort agénésie sternale subtotale avec ectopia cordis: gestion chirurgicale et résultat à long terme (à propos d´un cas au bénin)
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8498673/
https://www.ncbi.nlm.nih.gov/pubmed/34659606
http://dx.doi.org/10.11604/pamj.2021.39.233.25646
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