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Extracellular phosphate enhances the function of F508del-CFTR rescued by CFTR correctors
Background: The clinical response to cystic fibrosis transmembrane conductance regulator (CFTR) modulators varies between people with cystic fibrosis (CF) of the same genotype, in part through the action of solute carriers encoded by modifier genes. Here, we investigate whether phosphate transport b...
Autores principales: | Saint-Criq, Vinciane, Wang, Yiting, Delpiano, Livia, Lin, JinHeng, Sheppard, David N., Gray, Michael A. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8503924/ https://www.ncbi.nlm.nih.gov/pubmed/34020896 http://dx.doi.org/10.1016/j.jcf.2021.04.013 |
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