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Cellular Models for Primary CoQ Deficiency Pathogenesis Study

Primary coenzyme Q(10) (CoQ) deficiency includes a heterogeneous group of mitochondrial diseases characterized by low mitochondrial levels of CoQ due to decreased endogenous biosynthesis rate. These diseases respond to CoQ treatment mainly at the early stages of the disease. The advances in the next...

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Detalles Bibliográficos
Autores principales:	Santos-Ocaña, Carlos, Cascajo, María V., Alcázar-Fabra, María, Staiano, Carmine, López-Lluch, Guillermo, Brea-Calvo, Gloria, Navas, Plácido
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8508219/ https://www.ncbi.nlm.nih.gov/pubmed/34638552 http://dx.doi.org/10.3390/ijms221910211

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