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Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child

Trichobezoars are indigestible masses of ingested hair commonly found in the stomach, often presenting with symptoms related to gastric outlet obstruction and severity related to the mass’s size and location. Gastrointestinal complications include ulceration, perforation, peritonitis, pancreatitis,...

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Detalles Bibliográficos
Autores principales: Head, William T, Parrado, Raphael H, McDuffie, Lucas
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8510510/
https://www.ncbi.nlm.nih.gov/pubmed/34660106
http://dx.doi.org/10.7759/cureus.17911
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author Head, William T
Parrado, Raphael H
McDuffie, Lucas
author_facet Head, William T
Parrado, Raphael H
McDuffie, Lucas
author_sort Head, William T
collection PubMed
description Trichobezoars are indigestible masses of ingested hair commonly found in the stomach, often presenting with symptoms related to gastric outlet obstruction and severity related to the mass’s size and location. Gastrointestinal complications include ulceration, perforation, peritonitis, pancreatitis, obstructive jaundice, pneumatosis intestinalis, and intussusception. Management of trichobezoars differs from that of other forms of bezoars, which can often be addressed with chemical dissolution. Trichobezoars are high-density structures that are also resistant to enzymatic and pharmacotherapy degradation, and as such, they require endoscopic, or more commonly, surgical removal. Here, we present the diagnosis and surgical management of a 12-year-old female with a large trichobezoar causing gastric outlet obstruction, with an associated Rapunzel syndrome manifesting as multiple small intestinal intussusceptions.
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spelling pubmed-85105102021-10-15 Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child Head, William T Parrado, Raphael H McDuffie, Lucas Cureus Pediatrics Trichobezoars are indigestible masses of ingested hair commonly found in the stomach, often presenting with symptoms related to gastric outlet obstruction and severity related to the mass’s size and location. Gastrointestinal complications include ulceration, perforation, peritonitis, pancreatitis, obstructive jaundice, pneumatosis intestinalis, and intussusception. Management of trichobezoars differs from that of other forms of bezoars, which can often be addressed with chemical dissolution. Trichobezoars are high-density structures that are also resistant to enzymatic and pharmacotherapy degradation, and as such, they require endoscopic, or more commonly, surgical removal. Here, we present the diagnosis and surgical management of a 12-year-old female with a large trichobezoar causing gastric outlet obstruction, with an associated Rapunzel syndrome manifesting as multiple small intestinal intussusceptions. Cureus 2021-09-12 /pmc/articles/PMC8510510/ /pubmed/34660106 http://dx.doi.org/10.7759/cureus.17911 Text en Copyright © 2021, Head et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Pediatrics
Head, William T
Parrado, Raphael H
McDuffie, Lucas
Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child
title Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child
title_full Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child
title_fullStr Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child
title_full_unstemmed Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child
title_short Rapunzel Syndrome: A Rare Case of Small Bowel Intussusception in a Child
title_sort rapunzel syndrome: a rare case of small bowel intussusception in a child
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8510510/
https://www.ncbi.nlm.nih.gov/pubmed/34660106
http://dx.doi.org/10.7759/cureus.17911
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