Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome

We discuss an adolescent with Marfan syndrome and a previous aortic valve-sparing root replacement who was found to have mitral annular disjunction on surveillance cardiac imaging in the setting of recurrent palpitations. Ambulatory heart rate monitoring incidentally captured a fatal ventricular arr...

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Autores principales: Carr, Karen, Yetman, Anji, Garg, Ruchira
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8511475/
https://www.ncbi.nlm.nih.gov/pubmed/34693358
http://dx.doi.org/10.1016/j.jaccas.2021.08.006
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author Carr, Karen
Yetman, Anji
Garg, Ruchira
author_facet Carr, Karen
Yetman, Anji
Garg, Ruchira
author_sort Carr, Karen
collection PubMed
description We discuss an adolescent with Marfan syndrome and a previous aortic valve-sparing root replacement who was found to have mitral annular disjunction on surveillance cardiac imaging in the setting of recurrent palpitations. Ambulatory heart rate monitoring incidentally captured a fatal ventricular arrhythmia, a well-recognized but underappreciated cause of sudden cardiac death in patients with Marfan syndrome. (Level of Difficulty: Advanced.)
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spelling pubmed-85114752021-10-21 Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome Carr, Karen Yetman, Anji Garg, Ruchira JACC Case Rep Case Report We discuss an adolescent with Marfan syndrome and a previous aortic valve-sparing root replacement who was found to have mitral annular disjunction on surveillance cardiac imaging in the setting of recurrent palpitations. Ambulatory heart rate monitoring incidentally captured a fatal ventricular arrhythmia, a well-recognized but underappreciated cause of sudden cardiac death in patients with Marfan syndrome. (Level of Difficulty: Advanced.) Elsevier 2021-10-06 /pmc/articles/PMC8511475/ /pubmed/34693358 http://dx.doi.org/10.1016/j.jaccas.2021.08.006 Text en © 2021 The Authors https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Carr, Karen
Yetman, Anji
Garg, Ruchira
Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome
title Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome
title_full Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome
title_fullStr Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome
title_full_unstemmed Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome
title_short Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome
title_sort mitral annular disjunction associated with fatal ventricular arrhythmia in an adolescent with marfan syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8511475/
https://www.ncbi.nlm.nih.gov/pubmed/34693358
http://dx.doi.org/10.1016/j.jaccas.2021.08.006
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AT gargruchira mitralannulardisjunctionassociatedwithfatalventriculararrhythmiainanadolescentwithmarfansyndrome

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