Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas

Stiff person syndrome (SPS) is a rare disease affecting the central nervous system which can be autoimmune, paraneoplastic or idiopathic in origin. Its typical classic presentation is characterized by progressive stiffness of the trunk and limbs, associated with spasms. The diagnosis is supported by...

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Detalles Bibliográficos
Autores principales: Tayebi, Loubna, Keita, Ansumana Mohammed, Louhab, Nisrine, Zahlane, Mouna, Benjilali, Laila, Essaadouni, Lamiaa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8531973/
https://www.ncbi.nlm.nih.gov/pubmed/34733395
http://dx.doi.org/10.11604/pamj.2021.40.27.30313
Descripción
Sumario:Stiff person syndrome (SPS) is a rare disease affecting the central nervous system which can be autoimmune, paraneoplastic or idiopathic in origin. Its typical classic presentation is characterized by progressive stiffness of the trunk and limbs, associated with spasms. The diagnosis is supported by the existence of continuous and spontaneous muscle activity on electroneuromyogram detection, the presence of serum anti-GAD antibodies, and a response to benzodiazepines. We report the case of a 46-year-old patient with a classic form of autoimmune stiff person syndrome associated with dermatitis herpetiformis.

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