Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas

Stiff person syndrome (SPS) is a rare disease affecting the central nervous system which can be autoimmune, paraneoplastic or idiopathic in origin. Its typical classic presentation is characterized by progressive stiffness of the trunk and limbs, associated with spasms. The diagnosis is supported by...

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Autores principales: Tayebi, Loubna, Keita, Ansumana Mohammed, Louhab, Nisrine, Zahlane, Mouna, Benjilali, Laila, Essaadouni, Lamiaa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8531973/
https://www.ncbi.nlm.nih.gov/pubmed/34733395
http://dx.doi.org/10.11604/pamj.2021.40.27.30313
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author Tayebi, Loubna
Keita, Ansumana Mohammed
Louhab, Nisrine
Zahlane, Mouna
Benjilali, Laila
Essaadouni, Lamiaa
author_facet Tayebi, Loubna
Keita, Ansumana Mohammed
Louhab, Nisrine
Zahlane, Mouna
Benjilali, Laila
Essaadouni, Lamiaa
author_sort Tayebi, Loubna
collection PubMed
description Stiff person syndrome (SPS) is a rare disease affecting the central nervous system which can be autoimmune, paraneoplastic or idiopathic in origin. Its typical classic presentation is characterized by progressive stiffness of the trunk and limbs, associated with spasms. The diagnosis is supported by the existence of continuous and spontaneous muscle activity on electroneuromyogram detection, the presence of serum anti-GAD antibodies, and a response to benzodiazepines. We report the case of a 46-year-old patient with a classic form of autoimmune stiff person syndrome associated with dermatitis herpetiformis.
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spelling pubmed-85319732021-11-02 Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas Tayebi, Loubna Keita, Ansumana Mohammed Louhab, Nisrine Zahlane, Mouna Benjilali, Laila Essaadouni, Lamiaa Pan Afr Med J Case Report Stiff person syndrome (SPS) is a rare disease affecting the central nervous system which can be autoimmune, paraneoplastic or idiopathic in origin. Its typical classic presentation is characterized by progressive stiffness of the trunk and limbs, associated with spasms. The diagnosis is supported by the existence of continuous and spontaneous muscle activity on electroneuromyogram detection, the presence of serum anti-GAD antibodies, and a response to benzodiazepines. We report the case of a 46-year-old patient with a classic form of autoimmune stiff person syndrome associated with dermatitis herpetiformis. The African Field Epidemiology Network 2021-09-09 /pmc/articles/PMC8531973/ /pubmed/34733395 http://dx.doi.org/10.11604/pamj.2021.40.27.30313 Text en Copyright: Loubna Tayebi et al. https://creativecommons.org/licenses/by/4.0/The Pan African Medical Journal (ISSN: 1937-8688). This is an Open Access article distributed under the terms of the Creative Commons Attribution International 4.0 License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Tayebi, Loubna
Keita, Ansumana Mohammed
Louhab, Nisrine
Zahlane, Mouna
Benjilali, Laila
Essaadouni, Lamiaa
Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
title Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
title_full Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
title_fullStr Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
title_full_unstemmed Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
title_short Syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
title_sort syndrome de la personne raide associé à une dermatite herpétiforme: à propos d’un cas
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8531973/
https://www.ncbi.nlm.nih.gov/pubmed/34733395
http://dx.doi.org/10.11604/pamj.2021.40.27.30313
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