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Defining the Prion Type of Fatal Familial Insomnia

Fatal familial insomnia (FFI) belongs to the genetic human transmissible spongiform encephalopathies (TSE), such as genetic Creutzfeldt-Jakob disease (CJD) or Gerstmann-Straeussler-Scheinker syndrome (GSS). Here, we analyzed the properties of the pathological prion protein in six FFI cases by Wester...

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Detalles Bibliográficos
Autores principales:	Jürgens-Wemheuer, Wiebke, Wrede, Arne, Schulz-Schaeffer, Walter
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8539405/ https://www.ncbi.nlm.nih.gov/pubmed/34684242 http://dx.doi.org/10.3390/pathogens10101293

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