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The Effects of a Ketogenic Diet on Patients with Dihydrolipoamide Dehydrogenase Deficiency

Background: Dihydrolipoamide dehydrogenase (DLD lipoamide dehydrogenase, the E3 subunit of the pyruvate dehydrogenase complex (PDHC)) is the third catalytic enzyme of the PDHC, which converts pyruvate to acetyl-CoA catalyzed with the introduction of acetyl-CoA to the tricyclic acid (TCA) cycle. In h...

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Detalles Bibliográficos
Autores principales:	Staretz-Chacham, Orna, Pode-Shakked, Ben, Kristal, Eyal, Abraham, Smadar Yaala, Porper, Keren, Wormser, Ohad, Shelef, Ilan, Anikster, Yair
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8540285/ https://www.ncbi.nlm.nih.gov/pubmed/34684524 http://dx.doi.org/10.3390/nu13103523

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