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Mitochondrial disease, mitophagy, and cellular distress in methylmalonic acidemia

Mitochondria—the intracellular powerhouse in which nutrients are converted into energy in the form of ATP or heat—are highly dynamic, double-membraned organelles that harness a plethora of cellular functions that sustain energy metabolism and homeostasis. Exciting new discoveries now indicate that t...

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Detalles Bibliográficos
Autores principales:	Luciani, Alessandro, Denley, Matthew C. S., Govers, Larissa P., Sorrentino, Vincenzo, Froese, D. Sean
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Springer International Publishing 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8558192/ https://www.ncbi.nlm.nih.gov/pubmed/34524466 http://dx.doi.org/10.1007/s00018-021-03934-3

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