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Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-...
Autores principales: | , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Frontiers Media S.A.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8573143/ https://www.ncbi.nlm.nih.gov/pubmed/34760936 http://dx.doi.org/10.3389/fcvm.2021.709328 |
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author | Cossío-Aranda, Jorge Aranda-Frausto, Alberto Berarducci, Joaquin Espinola-Zavaleta, Nilda González-Melchor, Laila Vázquez-Antona, Clara Meléndez-Ramirez, Gabriela Armenta-Moreno, Javier Ivan Keirns, Candace |
author_facet | Cossío-Aranda, Jorge Aranda-Frausto, Alberto Berarducci, Joaquin Espinola-Zavaleta, Nilda González-Melchor, Laila Vázquez-Antona, Clara Meléndez-Ramirez, Gabriela Armenta-Moreno, Javier Ivan Keirns, Candace |
author_sort | Cossío-Aranda, Jorge |
collection | PubMed |
description | We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.” |
format | Online Article Text |
id | pubmed-8573143 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Frontiers Media S.A. |
record_format | MEDLINE/PubMed |
spelling | pubmed-85731432021-11-09 Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma Cossío-Aranda, Jorge Aranda-Frausto, Alberto Berarducci, Joaquin Espinola-Zavaleta, Nilda González-Melchor, Laila Vázquez-Antona, Clara Meléndez-Ramirez, Gabriela Armenta-Moreno, Javier Ivan Keirns, Candace Front Cardiovasc Med Cardiovascular Medicine We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.” Frontiers Media S.A. 2021-10-25 /pmc/articles/PMC8573143/ /pubmed/34760936 http://dx.doi.org/10.3389/fcvm.2021.709328 Text en Copyright © 2021 Cossío-Aranda, Aranda-Frausto, Berarducci, Espinola-Zavaleta, González-Melchor, Vázquez-Antona, Meléndez-Ramirez, Armenta-Moreno and Keirns. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms. |
spellingShingle | Cardiovascular Medicine Cossío-Aranda, Jorge Aranda-Frausto, Alberto Berarducci, Joaquin Espinola-Zavaleta, Nilda González-Melchor, Laila Vázquez-Antona, Clara Meléndez-Ramirez, Gabriela Armenta-Moreno, Javier Ivan Keirns, Candace Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
title | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
title_full | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
title_fullStr | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
title_full_unstemmed | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
title_short | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
title_sort | case report: a rare case of a ventricular perivascular epithelioid cell tumor with histologic characteristics that resembled a primary cardiac rhabdomyoma |
topic | Cardiovascular Medicine |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8573143/ https://www.ncbi.nlm.nih.gov/pubmed/34760936 http://dx.doi.org/10.3389/fcvm.2021.709328 |
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