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Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma

We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-...

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Autores principales: Cossío-Aranda, Jorge, Aranda-Frausto, Alberto, Berarducci, Joaquin, Espinola-Zavaleta, Nilda, González-Melchor, Laila, Vázquez-Antona, Clara, Meléndez-Ramirez, Gabriela, Armenta-Moreno, Javier Ivan, Keirns, Candace
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8573143/
https://www.ncbi.nlm.nih.gov/pubmed/34760936
http://dx.doi.org/10.3389/fcvm.2021.709328
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author Cossío-Aranda, Jorge
Aranda-Frausto, Alberto
Berarducci, Joaquin
Espinola-Zavaleta, Nilda
González-Melchor, Laila
Vázquez-Antona, Clara
Meléndez-Ramirez, Gabriela
Armenta-Moreno, Javier Ivan
Keirns, Candace
author_facet Cossío-Aranda, Jorge
Aranda-Frausto, Alberto
Berarducci, Joaquin
Espinola-Zavaleta, Nilda
González-Melchor, Laila
Vázquez-Antona, Clara
Meléndez-Ramirez, Gabriela
Armenta-Moreno, Javier Ivan
Keirns, Candace
author_sort Cossío-Aranda, Jorge
collection PubMed
description We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.”
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spelling pubmed-85731432021-11-09 Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma Cossío-Aranda, Jorge Aranda-Frausto, Alberto Berarducci, Joaquin Espinola-Zavaleta, Nilda González-Melchor, Laila Vázquez-Antona, Clara Meléndez-Ramirez, Gabriela Armenta-Moreno, Javier Ivan Keirns, Candace Front Cardiovasc Med Cardiovascular Medicine We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.” Frontiers Media S.A. 2021-10-25 /pmc/articles/PMC8573143/ /pubmed/34760936 http://dx.doi.org/10.3389/fcvm.2021.709328 Text en Copyright © 2021 Cossío-Aranda, Aranda-Frausto, Berarducci, Espinola-Zavaleta, González-Melchor, Vázquez-Antona, Meléndez-Ramirez, Armenta-Moreno and Keirns. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Cardiovascular Medicine
Cossío-Aranda, Jorge
Aranda-Frausto, Alberto
Berarducci, Joaquin
Espinola-Zavaleta, Nilda
González-Melchor, Laila
Vázquez-Antona, Clara
Meléndez-Ramirez, Gabriela
Armenta-Moreno, Javier Ivan
Keirns, Candace
Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
title Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
title_full Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
title_fullStr Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
title_full_unstemmed Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
title_short Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
title_sort case report: a rare case of a ventricular perivascular epithelioid cell tumor with histologic characteristics that resembled a primary cardiac rhabdomyoma
topic Cardiovascular Medicine
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8573143/
https://www.ncbi.nlm.nih.gov/pubmed/34760936
http://dx.doi.org/10.3389/fcvm.2021.709328
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