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Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review

Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐like pulmo...

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Autores principales: Luo, Tian, Wang, Lile, Fu, Daiyan, Hu, Ruicheng, Kong, Chunchu, Chen, Yunrong, Li, Xi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley & Sons, Ltd 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8573544/
https://www.ncbi.nlm.nih.gov/pubmed/34765226
http://dx.doi.org/10.1002/rcr2.873
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author Luo, Tian
Wang, Lile
Fu, Daiyan
Hu, Ruicheng
Kong, Chunchu
Chen, Yunrong
Li, Xi
author_facet Luo, Tian
Wang, Lile
Fu, Daiyan
Hu, Ruicheng
Kong, Chunchu
Chen, Yunrong
Li, Xi
author_sort Luo, Tian
collection PubMed
description Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐like pulmonary manifestation. However, such reports are rare in China. We report here a case of GS in China with DPB as the prominent manifestation and carry out a literature review accordingly. Our review indicates that in adults with DPB‐like clinical manifestations, thymic lesions should be excluded and related immune function tests should be performed to exclude GS to avoid missed diagnosis and misdiagnosis.
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spelling pubmed-85735442021-11-10 Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review Luo, Tian Wang, Lile Fu, Daiyan Hu, Ruicheng Kong, Chunchu Chen, Yunrong Li, Xi Respirol Case Rep Case Reports Good's syndrome (GS) is characterized by thymoma combined with adult‐onset immunodeficiency. Diffuse panbronchiolitis (DPB) is a chronic inflammatory airway disease, which predominantly affects East Asians. Japanese scholars have reported extensively about GS combined with DPB or DPB‐like pulmonary manifestation. However, such reports are rare in China. We report here a case of GS in China with DPB as the prominent manifestation and carry out a literature review accordingly. Our review indicates that in adults with DPB‐like clinical manifestations, thymic lesions should be excluded and related immune function tests should be performed to exclude GS to avoid missed diagnosis and misdiagnosis. John Wiley & Sons, Ltd 2021-11-08 /pmc/articles/PMC8573544/ /pubmed/34765226 http://dx.doi.org/10.1002/rcr2.873 Text en © 2021 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Reports
Luo, Tian
Wang, Lile
Fu, Daiyan
Hu, Ruicheng
Kong, Chunchu
Chen, Yunrong
Li, Xi
Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_full Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_fullStr Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_full_unstemmed Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_short Good's syndrome with diffuse panbronchiolitis as the prominent manifestation: A case and literature review
title_sort good's syndrome with diffuse panbronchiolitis as the prominent manifestation: a case and literature review
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8573544/
https://www.ncbi.nlm.nih.gov/pubmed/34765226
http://dx.doi.org/10.1002/rcr2.873
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