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LUBAC: a new player in polyglucosan body disease
Altered protein ubiquitination is associated with the pathobiology of numerous diseases; however, its involvement in glycogen metabolism and associated polyglucosan body (PB) disease has not been investigated in depth. In PB disease, excessively long and less branched glycogen chains (polyglucosan b...
Autores principales: | Aboujaoude, Andrew, Minassian, Berge, Mitra, Sharmistha |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Portland Press Ltd.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8589444/ https://www.ncbi.nlm.nih.gov/pubmed/34709403 http://dx.doi.org/10.1042/BST20210838 |
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