Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases

Langerhans cell histiocytosis (LCH) is a rare group of disorder, due to clonal neoplastic proliferation of dendritic cells in the bone marrow expressing a Langerhans cell phenotype. 1 This disease particularly affects the pediatric age group and young adults and often presents with skin rashes, lung...

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Autores principales: Pratap, Thara, Jalal, Muhammed Jasim Abdul, R., Rashmi, Gopalakrishnabhakthan, Anupama, AK, Vishnu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Medical and Scientific Publishers Pvt. Ltd. 2021
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8590574/
https://www.ncbi.nlm.nih.gov/pubmed/34790313
http://dx.doi.org/10.1055/s-0041-1735505
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author Pratap, Thara
Jalal, Muhammed Jasim Abdul
R., Rashmi
Gopalakrishnabhakthan, Anupama
AK, Vishnu
author_facet Pratap, Thara
Jalal, Muhammed Jasim Abdul
R., Rashmi
Gopalakrishnabhakthan, Anupama
AK, Vishnu
author_sort Pratap, Thara
collection PubMed
description Langerhans cell histiocytosis (LCH) is a rare group of disorder, due to clonal neoplastic proliferation of dendritic cells in the bone marrow expressing a Langerhans cell phenotype. 1 This disease particularly affects the pediatric age group and young adults and often presents with skin rashes, lung infiltrates, and bone lesions. It can also manifest with endocrine dysfunction and hematopoietic disorders. Involvement of gastrointestinal tract is very rare. Herein, we present a spectrum of three cases with gastrointestinal involvement.
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spelling pubmed-85905742021-11-16 Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases Pratap, Thara Jalal, Muhammed Jasim Abdul R., Rashmi Gopalakrishnabhakthan, Anupama AK, Vishnu Indian J Radiol Imaging Langerhans cell histiocytosis (LCH) is a rare group of disorder, due to clonal neoplastic proliferation of dendritic cells in the bone marrow expressing a Langerhans cell phenotype. 1 This disease particularly affects the pediatric age group and young adults and often presents with skin rashes, lung infiltrates, and bone lesions. It can also manifest with endocrine dysfunction and hematopoietic disorders. Involvement of gastrointestinal tract is very rare. Herein, we present a spectrum of three cases with gastrointestinal involvement. Thieme Medical and Scientific Publishers Pvt. Ltd. 2021-09-07 /pmc/articles/PMC8590574/ /pubmed/34790313 http://dx.doi.org/10.1055/s-0041-1735505 Text en Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. ( https://creativecommons.org/licenses/by-nc-nd/4.0/ ) https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial-NoDerivatives License, which permits unrestricted reproduction and distribution, for non-commercial purposes only; and use and reproduction, but not distribution, of adapted material for non-commercial purposes only, provided the original work is properly cited.
spellingShingle Pratap, Thara
Jalal, Muhammed Jasim Abdul
R., Rashmi
Gopalakrishnabhakthan, Anupama
AK, Vishnu
Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases
title Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases
title_full Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases
title_fullStr Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases
title_full_unstemmed Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases
title_short Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis—Spectrum of Three Cases
title_sort hepatobiliary and gastrointestinal involvement in langerhans cell histiocytosis—spectrum of three cases
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8590574/
https://www.ncbi.nlm.nih.gov/pubmed/34790313
http://dx.doi.org/10.1055/s-0041-1735505
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