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Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver
Undifferentiated embryonal sarcoma of the liver (UESL) is very rare and has a very poor prognosis. UESL metastases have been reported in 5%-13% of the children with UESL and most metastases reported in the literature are present at diagnosis. Metastases reported in the literature belong to the lungs...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8601971/ https://www.ncbi.nlm.nih.gov/pubmed/34820039 http://dx.doi.org/10.1016/j.radcr.2021.10.017 |
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author | Dogan, Gulec Mert Sığırcı, Ahmet Okut, Gokalp Dogan, Sait Murat Yilmaz, Sezai |
author_facet | Dogan, Gulec Mert Sığırcı, Ahmet Okut, Gokalp Dogan, Sait Murat Yilmaz, Sezai |
author_sort | Dogan, Gulec Mert |
collection | PubMed |
description | Undifferentiated embryonal sarcoma of the liver (UESL) is very rare and has a very poor prognosis. UESL metastases have been reported in 5%-13% of the children with UESL and most metastases reported in the literature are present at diagnosis. Metastases reported in the literature belong to the lungs, pleura, and peritoneum. Radiological diagnosis of the UESL remains a poorly understood problem due to its rarity. Most of the reports published in the literature are also based on a relatively small number of patients. Approximately 200 cases have been reported regarding imaging features of this tumor. We reported a girl with UESL, who applied to the emergency department with abdominal pain. The lesion was solid and had cystic areas on ultrasound and there were peripherally enhanced serpenginous vessels in the lesion on Computed Tomography and MRI. Immunohistochemical diagnosis of the lesion was UESL. 26 months after surgery and adjuvant chemotherapy extradural and subcutaneus metastases were detected. These metastasis sites were first described for UESL. |
format | Online Article Text |
id | pubmed-8601971 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-86019712021-11-23 Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver Dogan, Gulec Mert Sığırcı, Ahmet Okut, Gokalp Dogan, Sait Murat Yilmaz, Sezai Radiol Case Rep Case Report Undifferentiated embryonal sarcoma of the liver (UESL) is very rare and has a very poor prognosis. UESL metastases have been reported in 5%-13% of the children with UESL and most metastases reported in the literature are present at diagnosis. Metastases reported in the literature belong to the lungs, pleura, and peritoneum. Radiological diagnosis of the UESL remains a poorly understood problem due to its rarity. Most of the reports published in the literature are also based on a relatively small number of patients. Approximately 200 cases have been reported regarding imaging features of this tumor. We reported a girl with UESL, who applied to the emergency department with abdominal pain. The lesion was solid and had cystic areas on ultrasound and there were peripherally enhanced serpenginous vessels in the lesion on Computed Tomography and MRI. Immunohistochemical diagnosis of the lesion was UESL. 26 months after surgery and adjuvant chemotherapy extradural and subcutaneus metastases were detected. These metastasis sites were first described for UESL. Elsevier 2021-11-10 /pmc/articles/PMC8601971/ /pubmed/34820039 http://dx.doi.org/10.1016/j.radcr.2021.10.017 Text en © 2021 Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Dogan, Gulec Mert Sığırcı, Ahmet Okut, Gokalp Dogan, Sait Murat Yilmaz, Sezai Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
title | Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
title_full | Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
title_fullStr | Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
title_full_unstemmed | Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
title_short | Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
title_sort | subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8601971/ https://www.ncbi.nlm.nih.gov/pubmed/34820039 http://dx.doi.org/10.1016/j.radcr.2021.10.017 |
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