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Defective Toll-Like Receptors Driven B Cell Response in Hyper IgE Syndrome Patients With STAT3 Mutations

Autosomal dominant hyper-IgE syndrome (AD-HIES) is a rare inherited primary immunodeficient disease (PIDs), which is caused by STAT3 gene mutations. Previous studies indicated a defective Toll-like receptor (TLR) 9-induced B cell response in AD-HIES patients, including proliferation, and IgG product...

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Detalles Bibliográficos
Autores principales:	Gong, Ruolan, Wu, Jing, Jin, Yingying, Chen, Tongxin
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2021
Materias:	Pediatrics
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8604043/ https://www.ncbi.nlm.nih.gov/pubmed/34805040 http://dx.doi.org/10.3389/fped.2021.738799

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