Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report

Acute disseminated encephalomyelitis (ADEM) is an immune-mediated demyelinating central nervous system disorder with predilection for early childhood. Delayed onset of ADEM is rare, and herein we present a previously healthy 5-year-old boy, with an unusual clinical course of ADEM with high intracran...

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Autores principales: Liminga, Gunnar, Grabowska, Anna, Pétursdóttir, Dýrleif, Cesarini, Kristina G., Rostami, Elham, Ehrstedt, Christoffer
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Berlin Heidelberg 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8604833/
https://www.ncbi.nlm.nih.gov/pubmed/34136944
http://dx.doi.org/10.1007/s00381-021-05188-7
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author Liminga, Gunnar
Grabowska, Anna
Pétursdóttir, Dýrleif
Cesarini, Kristina G.
Rostami, Elham
Ehrstedt, Christoffer
author_facet Liminga, Gunnar
Grabowska, Anna
Pétursdóttir, Dýrleif
Cesarini, Kristina G.
Rostami, Elham
Ehrstedt, Christoffer
author_sort Liminga, Gunnar
collection PubMed
description Acute disseminated encephalomyelitis (ADEM) is an immune-mediated demyelinating central nervous system disorder with predilection for early childhood. Delayed onset of ADEM is rare, and herein we present a previously healthy 5-year-old boy, with an unusual clinical course of ADEM with high intracranial pressure (ICP) and acute visual loss that was at first diagnosed as idiopathic intracranial hypertension without papilledema (IIHWOP). The boy underwent acute neurosurgical intervention with ventriculoperitoneal (VP) shunt using Miethke valve and sensor reservoir system and received high-dose steroid treatment with symptom relieve within days. This is the first case report using this system in such a young child, and we find it feasible and valuable also in younger children when VP shunt with ICP measurement is indicated.
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spelling pubmed-86048332021-12-03 Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report Liminga, Gunnar Grabowska, Anna Pétursdóttir, Dýrleif Cesarini, Kristina G. Rostami, Elham Ehrstedt, Christoffer Childs Nerv Syst Case Report Acute disseminated encephalomyelitis (ADEM) is an immune-mediated demyelinating central nervous system disorder with predilection for early childhood. Delayed onset of ADEM is rare, and herein we present a previously healthy 5-year-old boy, with an unusual clinical course of ADEM with high intracranial pressure (ICP) and acute visual loss that was at first diagnosed as idiopathic intracranial hypertension without papilledema (IIHWOP). The boy underwent acute neurosurgical intervention with ventriculoperitoneal (VP) shunt using Miethke valve and sensor reservoir system and received high-dose steroid treatment with symptom relieve within days. This is the first case report using this system in such a young child, and we find it feasible and valuable also in younger children when VP shunt with ICP measurement is indicated. Springer Berlin Heidelberg 2021-06-16 2021 /pmc/articles/PMC8604833/ /pubmed/34136944 http://dx.doi.org/10.1007/s00381-021-05188-7 Text en © The Author(s) 2021 https://creativecommons.org/licenses/by/4.0/Open Access This article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) .
spellingShingle Case Report
Liminga, Gunnar
Grabowska, Anna
Pétursdóttir, Dýrleif
Cesarini, Kristina G.
Rostami, Elham
Ehrstedt, Christoffer
Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report
title Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report
title_full Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report
title_fullStr Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report
title_full_unstemmed Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report
title_short Acute disseminated encephalomyelitis with delayed onset and feasibility of the Miethke shunt and sensor reservoir system: a case report
title_sort acute disseminated encephalomyelitis with delayed onset and feasibility of the miethke shunt and sensor reservoir system: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8604833/
https://www.ncbi.nlm.nih.gov/pubmed/34136944
http://dx.doi.org/10.1007/s00381-021-05188-7
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