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Beneficial Effects of Slow-Release Large Neutral Amino Acids after a Phenylalanine Oral Load in Patients with Phenylketonuria

The mainstay of phenylketonuria treatment is a low protein diet, supplemented with phenylalanine (Phe)-free protein substitutes and micronutrients. Adhering to this diet is challenging, and even patients with good metabolic control who follow the dietary prescriptions in everyday life ignore the rec...

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Detalles Bibliográficos
Autores principales:	Scala, Iris, Concolino, Daniela, Nastasi, Anna, Esposito, Giulia, Crisci, Daniela, Sestito, Simona, Ferraro, Stefania, Albano, Lucia, Ruoppolo, Margherita, Parenti, Giancarlo, Strisciuglio, Pietro
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8618154/ https://www.ncbi.nlm.nih.gov/pubmed/34836270 http://dx.doi.org/10.3390/nu13114012

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