Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease

Congenital Bochdalek hernia (BH) in an adult is rare and has an unusual presentation. They are confined to the pediatric age group with an incidence of 1:3,000 live births. It rarely persists asymptomatic until adulthood. Surgical repair by thoracic, abdominal, or thoraco-abdominal approach is the t...

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Autores principales: Dantis, Klein, Rathore, Devendra Kumar, Gupta, Nilesh, Singha, Subrata Kumar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Medical Publishers, Inc. 2021
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8702300/
https://www.ncbi.nlm.nih.gov/pubmed/34966850
http://dx.doi.org/10.1055/s-0041-1740628
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author Dantis, Klein
Rathore, Devendra Kumar
Gupta, Nilesh
Singha, Subrata Kumar
author_facet Dantis, Klein
Rathore, Devendra Kumar
Gupta, Nilesh
Singha, Subrata Kumar
author_sort Dantis, Klein
collection PubMed
description Congenital Bochdalek hernia (BH) in an adult is rare and has an unusual presentation. They are confined to the pediatric age group with an incidence of 1:3,000 live births. It rarely persists asymptomatic until adulthood. Surgical repair by thoracic, abdominal, or thoraco-abdominal approach is the treatment of choice with diaphragmatic reconstruction in associated diaphragmatic agenesis. With only 10 cases of BH with partial diaphragmatic agenesis reported to date, we discuss the rarity, unusual presentation, and management of BH in a young adult with sickle cell disease that has not been reported in the literature.
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spelling pubmed-87023002021-12-28 Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease Dantis, Klein Rathore, Devendra Kumar Gupta, Nilesh Singha, Subrata Kumar Surg J (N Y) Congenital Bochdalek hernia (BH) in an adult is rare and has an unusual presentation. They are confined to the pediatric age group with an incidence of 1:3,000 live births. It rarely persists asymptomatic until adulthood. Surgical repair by thoracic, abdominal, or thoraco-abdominal approach is the treatment of choice with diaphragmatic reconstruction in associated diaphragmatic agenesis. With only 10 cases of BH with partial diaphragmatic agenesis reported to date, we discuss the rarity, unusual presentation, and management of BH in a young adult with sickle cell disease that has not been reported in the literature. Thieme Medical Publishers, Inc. 2021-12-23 /pmc/articles/PMC8702300/ /pubmed/34966850 http://dx.doi.org/10.1055/s-0041-1740628 Text en The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. ( https://creativecommons.org/licenses/by/4.0/ ) https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Dantis, Klein
Rathore, Devendra Kumar
Gupta, Nilesh
Singha, Subrata Kumar
Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease
title Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease
title_full Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease
title_fullStr Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease
title_full_unstemmed Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease
title_short Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease
title_sort bochdalek hernia and partial diaphragmatic agenesis: pedicled intercostal muscle flap and mesh repair in a young adult with sickle cell disease
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8702300/
https://www.ncbi.nlm.nih.gov/pubmed/34966850
http://dx.doi.org/10.1055/s-0041-1740628
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