Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report

Diffuse pulmonary lymphangiomatosis (DPL), an exceptionally rare disease, mainly occurs in children and young adults of both sexes. Even though DPL is considered to be a benign disease, its prognosis is relatively poor. Because of its rarity, little guidance on diagnosis and treatment is available,...

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Autores principales: Dimiene, Ieva, Bieksiene, Kristina, Zaveckiene, Jurgita, Andrulis, Mindaugas, Optazaite, Daiva-Elzbieta, Vaguliene, Neringa, Zemaitis, Marius, Miliauskas, Skaidrius
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8706407/
https://www.ncbi.nlm.nih.gov/pubmed/34946253
http://dx.doi.org/10.3390/medicina57121308
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author Dimiene, Ieva
Bieksiene, Kristina
Zaveckiene, Jurgita
Andrulis, Mindaugas
Optazaite, Daiva-Elzbieta
Vaguliene, Neringa
Zemaitis, Marius
Miliauskas, Skaidrius
author_facet Dimiene, Ieva
Bieksiene, Kristina
Zaveckiene, Jurgita
Andrulis, Mindaugas
Optazaite, Daiva-Elzbieta
Vaguliene, Neringa
Zemaitis, Marius
Miliauskas, Skaidrius
author_sort Dimiene, Ieva
collection PubMed
description Diffuse pulmonary lymphangiomatosis (DPL), an exceptionally rare disease, mainly occurs in children and young adults of both sexes. Even though DPL is considered to be a benign disease, its prognosis is relatively poor. Because of its rarity, little guidance on diagnosis and treatment is available, which makes working with patients with DPL challenging for clinicians. We present here a case of a young man with DPL in whom treatment with sirolimus and propranolol rapidly achieved positive radiological and clinical effects.
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spelling pubmed-87064072021-12-25 Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report Dimiene, Ieva Bieksiene, Kristina Zaveckiene, Jurgita Andrulis, Mindaugas Optazaite, Daiva-Elzbieta Vaguliene, Neringa Zemaitis, Marius Miliauskas, Skaidrius Medicina (Kaunas) Case Report Diffuse pulmonary lymphangiomatosis (DPL), an exceptionally rare disease, mainly occurs in children and young adults of both sexes. Even though DPL is considered to be a benign disease, its prognosis is relatively poor. Because of its rarity, little guidance on diagnosis and treatment is available, which makes working with patients with DPL challenging for clinicians. We present here a case of a young man with DPL in whom treatment with sirolimus and propranolol rapidly achieved positive radiological and clinical effects. MDPI 2021-11-29 /pmc/articles/PMC8706407/ /pubmed/34946253 http://dx.doi.org/10.3390/medicina57121308 Text en © 2021 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Dimiene, Ieva
Bieksiene, Kristina
Zaveckiene, Jurgita
Andrulis, Mindaugas
Optazaite, Daiva-Elzbieta
Vaguliene, Neringa
Zemaitis, Marius
Miliauskas, Skaidrius
Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report
title Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report
title_full Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report
title_fullStr Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report
title_full_unstemmed Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report
title_short Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report
title_sort effective initial treatment of diffuse pulmonary lymphangiomatosis with sirolimus and propranolol: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8706407/
https://www.ncbi.nlm.nih.gov/pubmed/34946253
http://dx.doi.org/10.3390/medicina57121308
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