Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review

Fibrosing mediastinitis (FM) is a rare fibroinflammatory disease of the mediastinum with an etiology and clinical features that vary by world region. The characteristics of FM in Japan are still unknown. We herein report two Japanese patients with FM who were treated with corticosteroids and respond...

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Autores principales: Kobayashi, Yoichi, Ishiguro, Takashi, Takaku, Yotaro, Kagiyama, Naho, Shimizu, Yoshihiko, Takayanagi, Noboru
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Internal Medicine 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8710366/
https://www.ncbi.nlm.nih.gov/pubmed/34024847
http://dx.doi.org/10.2169/internalmedicine.5737-20
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author Kobayashi, Yoichi
Ishiguro, Takashi
Takaku, Yotaro
Kagiyama, Naho
Shimizu, Yoshihiko
Takayanagi, Noboru
author_facet Kobayashi, Yoichi
Ishiguro, Takashi
Takaku, Yotaro
Kagiyama, Naho
Shimizu, Yoshihiko
Takayanagi, Noboru
author_sort Kobayashi, Yoichi
collection PubMed
description Fibrosing mediastinitis (FM) is a rare fibroinflammatory disease of the mediastinum with an etiology and clinical features that vary by world region. The characteristics of FM in Japan are still unknown. We herein report two Japanese patients with FM who were treated with corticosteroids and responded well. We also reviewed the Japanese literature on PubMed(Ⓡ) and summarized the characteristics of 27 Japanese FM patients, including our two patients. In Japan, the predominant cases were those without a specific cause, were diffusely distributed, and responded well to corticosteroid therapy.
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spelling pubmed-87103662022-01-25 Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review Kobayashi, Yoichi Ishiguro, Takashi Takaku, Yotaro Kagiyama, Naho Shimizu, Yoshihiko Takayanagi, Noboru Intern Med Case Report Fibrosing mediastinitis (FM) is a rare fibroinflammatory disease of the mediastinum with an etiology and clinical features that vary by world region. The characteristics of FM in Japan are still unknown. We herein report two Japanese patients with FM who were treated with corticosteroids and responded well. We also reviewed the Japanese literature on PubMed(Ⓡ) and summarized the characteristics of 27 Japanese FM patients, including our two patients. In Japan, the predominant cases were those without a specific cause, were diffusely distributed, and responded well to corticosteroid therapy. The Japanese Society of Internal Medicine 2021-05-22 2021-12-01 /pmc/articles/PMC8710366/ /pubmed/34024847 http://dx.doi.org/10.2169/internalmedicine.5737-20 Text en Copyright © 2021 by The Japanese Society of Internal Medicine https://creativecommons.org/licenses/by-nc-nd/4.0/The Internal Medicine is an Open Access journal distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Kobayashi, Yoichi
Ishiguro, Takashi
Takaku, Yotaro
Kagiyama, Naho
Shimizu, Yoshihiko
Takayanagi, Noboru
Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review
title Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review
title_full Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review
title_fullStr Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review
title_full_unstemmed Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review
title_short Clinical Features of Fibrosing Mediastinitis in Japanese Patients: Two Case Reports and a Literature Review
title_sort clinical features of fibrosing mediastinitis in japanese patients: two case reports and a literature review
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8710366/
https://www.ncbi.nlm.nih.gov/pubmed/34024847
http://dx.doi.org/10.2169/internalmedicine.5737-20
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