Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon

The authors present a rare case of a patient with telangiectasia macular eruptiva perstans, with confirmed D816V mutation which later progressed to systemic mastocytosis confirmed by trepanobiopsy. First-line treatment − phototherapy − had to be stopped, and systemic treatment with interferon alpha-...

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Detalles Bibliográficos
Autores principales: Péčová, Tatiana, Burjanivová, Tatiana, Malicherová, Bibiana, Péč, Martin Jozef, Rohoň, Igor, Madleňák, Matúš, Adamicová, Katarína, Péč, Juraj
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2021
Materias:
Single Case
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8740000/
https://www.ncbi.nlm.nih.gov/pubmed/35082619
http://dx.doi.org/10.1159/000520533
Descripción
Sumario:The authors present a rare case of a patient with telangiectasia macular eruptiva perstans, with confirmed D816V mutation which later progressed to systemic mastocytosis confirmed by trepanobiopsy. First-line treatment − phototherapy − had to be stopped, and systemic treatment with interferon alpha-2a was initiated. The treatment was successful with regression of skin lesions as well as mast cell infiltrates in the bone marrow. However, the treatment was complicated by the onset of psoriasis lesions.

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