Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon

The authors present a rare case of a patient with telangiectasia macular eruptiva perstans, with confirmed D816V mutation which later progressed to systemic mastocytosis confirmed by trepanobiopsy. First-line treatment − phototherapy − had to be stopped, and systemic treatment with interferon alpha-...

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Autores principales: Péčová, Tatiana, Burjanivová, Tatiana, Malicherová, Bibiana, Péč, Martin Jozef, Rohoň, Igor, Madleňák, Matúš, Adamicová, Katarína, Péč, Juraj
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2021
Materias:
Single Case
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8740000/
https://www.ncbi.nlm.nih.gov/pubmed/35082619
http://dx.doi.org/10.1159/000520533
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author Péčová, Tatiana
Burjanivová, Tatiana
Malicherová, Bibiana
Péč, Martin Jozef
Rohoň, Igor
Madleňák, Matúš
Adamicová, Katarína
Péč, Juraj
author_facet Péčová, Tatiana
Burjanivová, Tatiana
Malicherová, Bibiana
Péč, Martin Jozef
Rohoň, Igor
Madleňák, Matúš
Adamicová, Katarína
Péč, Juraj
author_sort Péčová, Tatiana
collection PubMed
description The authors present a rare case of a patient with telangiectasia macular eruptiva perstans, with confirmed D816V mutation which later progressed to systemic mastocytosis confirmed by trepanobiopsy. First-line treatment − phototherapy − had to be stopped, and systemic treatment with interferon alpha-2a was initiated. The treatment was successful with regression of skin lesions as well as mast cell infiltrates in the bone marrow. However, the treatment was complicated by the onset of psoriasis lesions.
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spelling pubmed-87400002022-01-25 Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon Péčová, Tatiana Burjanivová, Tatiana Malicherová, Bibiana Péč, Martin Jozef Rohoň, Igor Madleňák, Matúš Adamicová, Katarína Péč, Juraj Case Rep Dermatol Single Case The authors present a rare case of a patient with telangiectasia macular eruptiva perstans, with confirmed D816V mutation which later progressed to systemic mastocytosis confirmed by trepanobiopsy. First-line treatment − phototherapy − had to be stopped, and systemic treatment with interferon alpha-2a was initiated. The treatment was successful with regression of skin lesions as well as mast cell infiltrates in the bone marrow. However, the treatment was complicated by the onset of psoriasis lesions. S. Karger AG 2021-12-07 /pmc/articles/PMC8740000/ /pubmed/35082619 http://dx.doi.org/10.1159/000520533 Text en Copyright © 2021 by S. Karger AG, Basel https://creativecommons.org/licenses/by-nc/4.0/This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Single Case
Péčová, Tatiana
Burjanivová, Tatiana
Malicherová, Bibiana
Péč, Martin Jozef
Rohoň, Igor
Madleňák, Matúš
Adamicová, Katarína
Péč, Juraj
Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon
title Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon
title_full Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon
title_fullStr Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon
title_full_unstemmed Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon
title_short Newly Developed Psoriasis in a Patient with Telangiectasia Macularis Eruptiva Perstans and Systemic Mastocytosis Treated with Interferon
title_sort newly developed psoriasis in a patient with telangiectasia macularis eruptiva perstans and systemic mastocytosis treated with interferon
topic Single Case
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8740000/
https://www.ncbi.nlm.nih.gov/pubmed/35082619
http://dx.doi.org/10.1159/000520533
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